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 Heart block is a problem that occurs with the heart's electrical system. This system controls the rate and rhythm of heartbeats. ("Rate" refers to the number of times your heart beats per minute. "Rhythm" refers to the pattern of regular or irregular pulses produced as the heart beats.) With each heartbeat, an electrical signal spreads across the heart from the upper to the lower chambers. As it travels, the signal causes the heart to contract and pump blood. Heart block occurs if the electrical signal is slowed or disrupted as it moves through the heart. You can read this and more about heart block at the National Heart Lung and Blood Institute's Web site by clicking here.Lenegre disease is a familial form of progressive heart block.
Last updated: 5/13/2013
- Sauer WH. Etiology of atrioventricular block. In: Basow, DS. UpToDate. Waltham, MA: UpToDate; 2013;
- What is Heart Block?. National Heart, Lung and Blood Institute. http://www.nhlbi.nih.gov/health/health-topics/topics/hb/. Accessed 5/13/2013.
- How is Heart Block Treated?. National Heart, Lung and Blood Institute. http://www.nhlbi.nih.gov/health/health-topics/topics/hb/treated.html. Accessed 5/13/2013.
- Probst V et al.,. Haploinsufficiency in combination with aging causes SCN5A-linked hereditary Lenègre disease. J Am Coll Cardiol. 2003 Feb 19;41(4):643-52; http://www.ncbi.nlm.nih.gov/pubmed/?term=12598077. Accessed 5/13/2013.
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