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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Sickle beta thalassemia


Other Names for this Disease

  • Hb S beta-thalassemia
  • Hemoglobin sickle-beta thalassemia
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Treatment

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How might sickle beta thalassemia be treated?

Treatment for sickle beta thalassemia is supportive and usually depends on the signs and symptoms present in each person. It is generally recommended that all affected people drink plenty of water; avoid climate extremes, activities that lead to inflammation and extreme fatigue; and stay up-to-date on all immunizations. Because sickle beta thalassemia is associated with a variety of health problems, affected people are usually followed closely by their healthcare provider with regular physical examinations that may include specialized laboratory tests and imaging studies (i.e. chest X-ray, transcranial doppler ultrasound, ECG). Blood transfusions may be prescribed on a regular basis for affected people with a history or risk factors for stroke and other specific health problems, such as pulmonary hypertension. Hydroxyurea, a drug approved by the U.S. Food and Drug Administration for the treatment of sickle cell disease, can decrease the frequency and severity of pain episodes; reduce the need of blood transfusions; and increase life span.[1][2]

For more information regarding the treatment of sickle beta thalassemia and other sickle cell diseases, please click here.

Last updated: 12/22/2014

References
  1. MA Bender, MD, PhD and Gabrielle Douthitt Seibel, MN, MPH, ARNP. Sickle Cell Disease. GeneReviews. October 2014; http://www.ncbi.nlm.nih.gov/books/NBK1377/.
  2. Sickle Cell Disease. NORD. April 2008; https://www.rarediseases.org/rare-disease-information/rare-diseases/byID/25/viewAbstract.


Clinical Trials & Research for this Disease

  • ClinicalTrials.gov lists trials that are studying or have studied Sickle beta thalassemia. Click on the link to go to ClinicalTrials.gov to read descriptions of these studies.
Other Names for this Disease
  • Hb S beta-thalassemia
  • Hemoglobin sickle-beta thalassemia
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.