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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Craniopharyngioma


Other Names for this Disease
  • Adamantinoma
  • Adamantinomatous tumor
  • Craniopharyngeal duct tumor
  • Dysodontogenic epithelial tumor
  • Rathke's pouch tumor
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Overview


A craniopharyngioma is a slow-growing benign tumor that develops near the pituitary gland (a small endocrine gland at the base of the brain) and the hypothalamus (a small cone-shaped organ connected to the pituitary gland by nerves).[1][2][3] This tumor most commonly affects children between 5 and 10 years of age; however, adults can sometimes be affected.[1] Craniopharyngiomas are thought to arise from remnants of the craniopharyngeal duct and/or Rathke cleft or from metaplasia (abnormal transformation of cells) of squamous epithelial cell remnants of the stomadeum.[orphanet] Craniopharyngioma is treated with surgery alone or by surgery followed by radiation.[4]

Last updated: 4/3/2009

References

  1. Blackman S. Craniopharyngioma. MedlinePlus. 2004; http://www.nlm.nih.gov/medlineplus/ency/article/000345.htm. Accessed 4/3/2009.
  2. General Information About Childhood Craniopharyngioma. National Cancer Institute (NCI). 2009; http://www.cancer.gov/cancertopics/pdq/treatment/child-cranio/Patient. Accessed 4/3/2009.
  3. Garnett MR, Puget S, Grill J, Sainte-Rose C. Craniopharyngioma. Orphanet. 2007; http://www.orpha.net/consor/cgi-bin/Disease_Search.php?lng=EN&data_id=10756&Disease_Disease_Search_diseaseGroup=craniopharyngioma&Disease_Disease_Search_diseaseType=Pat&Disease(s)%20concerned=Craniopharyngioma&title=Craniopharyngioma&search=Disease_Search_Simple. Accessed 4/3/2009.
  4. Bobustuc GC, Groves MD, Fuller GN, DeMonte FN. Craniopharyngioma: Treatment & Medication. eMedicine. 2006; http://emedicine.medscape.com/article/1157758-treatment. Accessed 4/3/2009.
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Basic Information

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In Depth Information

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  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Craniopharyngioma. Click on the link to view a sample search on this topic.