Juvenile amyotrophic lateral sclerosis
Other Names for this Disease
- Amyotrophic lateral sclerosis, juvenile
- Amyotrophic lateral sclerosis type 2
- Amyotrophic lateral sclerosis type 4
- Amyotrophic lateral sclerosis type 5
What are the signs and symptoms of juvenile amyotrophic lateral sclerosis?
What causes juvenile amyotrophic lateral sclerosis?
How might juvenile amyotrophic lateral sclerosis be treated?
Juvenile amyotrophic lateral sclerosis (ALS) is a type of motor neuron disease which leads to problems with muscle control and movement. Signs and symptoms of juvenile ALS tend to present by age 25 years or younger. Unlike other types of ALS, juvenile ALS is not rapidly progressive. People with juvenile ALS can have a normal life expectancy. Juvenile ALS is often genetic and may be inherited in an autosomal dominant or autosomal recessive fashion.
While the Food and Drug Administration (FDA) has approved riluzole (Rilutek) for treatment of ALS, we found limited information regarding its use for juvenile ALS. We recommend that you discuss any questions regarding the risk/benefits of this drug with your healthcare provider.
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