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Juvenile amyotrophic lateral sclerosis
Other Names for this Disease
- Amyotrophic lateral sclerosis, juvenile
- Amyotrophic lateral sclerosis type 2
- Amyotrophic lateral sclerosis type 4
- Amyotrophic lateral sclerosis type 5
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Signs and symptoms of juvenile ALS vary but include slowly to very slowly progressive muscle weakness, increased muscle tone, Babinski reflex, muscle spasm (clonus), exaggerated reflexes, muscle wasting, and muscle twitching. Juvenile ALS usually does not affect thinking or mental processing, nor does it tend to cause sensory dysfunction (e.g., numbness or tingling). As the condition progresses muscle involvement can be severe. Some people with juvenile ALS, eventually experience muscle weakness in the face and throat. Some have experienced emotional liability (involuntary crying or laughing) and/or respiratory weakness.
Last updated: 7/8/2013
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