Your browser does not support javascript:   Search for gard hereSearch for news-and-events here.


Genetic and Rare Diseases Information Center (GARD)

Print friendly version

Hyper-IgD syndrome

Other Names for this Disease
  • Hyper IgD syndrome
  • Hyperimmunoglobulinemia D and periodic fever syndrome
  • Periodic fever Dutch type
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.


Newline Maker

What is the prognosis for individuals with hyper IgD syndrome?

Patients with hyper IgD syndrome have a good prognosis because amyloidosis has not been reported in any patient with this syndrome. No apparent neurologic or morphologic abnormalities occur, and, between fever attacks, patients are generally free of symptoms. Attacks do continue throughout the lifetime, although there may be a slight decrease following adolescence.[1]
Last updated: 3/5/2013

  1. Shinawi M, Scaglia F. Hereditary Periodic Fever Syndromes. Medscape Reference. 2013; Accessed 3/5/2013.