Your browser does not support javascript:   Search for gard hereSearch for news-and-events here.

Diseases

Genetic and Rare Diseases Information Center (GARD)

Print friendly version

Choroid plexus papilloma


Other Names for this Disease
  • Papilloma of choroid plexus
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Overview


Choroid plexus papilloma (CPP) ia a non-cancerous (benign) tumor of the choroid plexus, a network of blood vessels in the brain which surrounds the ventricles and produces the fluid surrounding the brain and spinal cord (cerebrospinal fluid, or CSF).[1] CPPs most commonly occur in children but may occur in adults.[2] Symptoms are generally due to increased secretion of CSF by tumor cells, causing hydrocephalus and subsequent intracranial pressure.[2] Affected individuals may experience headaches, nausea and vomiting, drowsiness, ocular or gaze palsies, optic nerve swelling (papilledema), visual disturbances, and possible blindness. Infants, especially those with a tumor in the third ventricle, can present with hydrocephalus or macrocephaly.[2] Some cases of CPP may result from a mutation in the TP53 gene.[3] Complete tumor removal often cures the condition and may also relieve the hydrocephalus.[1]
Last updated: 12/10/2012

References

  1. Choroid Plexus. American Brain Tumor Association. 2012; http://www.abta.org/understanding-brain-tumors/types-of-tumors/choroid-plexus.html. Accessed 12/10/2012.
  2. Cheryl Ann Palmer. Choroid Plexus Papilloma. Medscape Reference. March 8, 2012; http://emedicine.medscape.com/article/250795-overview. Accessed 12/10/2012.
  3. Papilloma of Choroid Plexus. OMIM. August 21, 2002; http://omim.org/entry/260500. Accessed 12/10/2012.
Your Questions Answered
by the Genetic and Rare Diseases Information Center

1 question(s) from the public on Choroid plexus papilloma have been answered. See questions and answers. You can also submit a new question.

Basic Information

  • The National Cancer Institute provides the most current information on cancer for patients, health professionals, and the general public.  Click on the link to view information on this topic. 

In Depth Information

  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • The Online Mendelian Inheritance in Man (OMIM) is an catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Choroid plexus papilloma. Click on the link to view a sample search on this topic.