Other Names for this Disease
- Congenital bronchopulmonary sequestration
- Congenital pulmonary sequestration
 It may be congenital (present from birth) or acquired. Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. Symptoms may include chronic cough, respiratory distress or infection. Treatment depends on the location and may involve surgery.Pulmonary sequestration is a rare malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation.
Last updated: 4/6/2010
- Pikwer A, Gyllstedt E, Lillo-Gil R, et al.. Scand J Surg. 2006; http://www.ncbi.nlm.nih.gov/pubmed/17066616. Accessed 4/6/2010.
- Khan AN, Aird M, Chiphang A, et al.. Pulmonary Sequestration. eMedicine. 2008; http://emedicine.medscape.com/article/412554-overview. Accessed 4/6/2010.
- Kliegman. Chapter 392 - Congenital Disorders of the Lung. In: Finder JD, Michelson PH. Nelson Textbook of Pediatrics, 18th ed.. Saunders; 2007;
- Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
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- eMedicine has two articles on this topic from the perspective of Pediatrics and Radiology. You may need to register to view the information online, but registration is free. Click on the links above to view the articles from this medical reference Web site.