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Pulmonary sequestration

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Pulmonary sequestration is a rare malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation.[1][2] It may be congenital (present from birth) or acquired.[2] Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location.[2][3] Symptoms may include chronic cough, respiratory distress or infection. Treatment depends on the location and may involve surgery.[2]
Last updated: 4/6/2010


  1. Pikwer A, Gyllstedt E, Lillo-Gil R, et al.. Scand J Surg. 2006; Accessed 4/6/2010.
  2. Khan AN, Aird M, Chiphang A, et al.. Pulmonary Sequestration. eMedicine. 2008; Accessed 4/6/2010.
  3. Kliegman. Chapter 392 - Congenital Disorders of the Lung. In: Finder JD, Michelson PH. Nelson Textbook of Pediatrics, 18th ed.. Saunders; 2007;
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  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.
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