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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Hereditary neuropathy with liability to pressure palsy


Other Names for this Disease
  • HNPP
  • Polyneuropathy, familial recurrent
  • Tomaculous neuropathy
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Your Question

What treatments are available for hereditary neuropathy with liability to pressure palsy?

Our Answer

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What treatments are available for hereditary neuropathy with liability to pressure palsy?

There is no specific treatment for hereditary neuropathy with liability to pressure palsy. Treatment is based on an individual's symptoms. Some people with this condition use braces, such as a wrist splint or ankle-foot orthosis (AFO). Protective pads worn at the elbows or knees may prevent pressure and trauma to local nerves. Activities to avoid include prolonged sitting with legs crossed, occupations requiring repetitive movements of the wrist, prolonged leaning on elbows, and rapid weight loss. Vincristine, commonly used in the treatment of lymphoma, has been reported to worsen the symptoms of hereditary neuropathy with liability to pressure palsy. Surgical decompression of nerves remains a controversial treament for this condition.[1]

Last updated: 7/20/2009

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