Dentinogenesis imperfecta 1
Other Names for this Disease
- Capdepont teeth
- Dentinogenesis imperfecta Shields type 2
- Dentinogenesis imperfecta type 1
- Dentinogenesis imperfecta without osteogenesis imperfecta
- Opalescent dentin
What causes dentinogenesis imperfecta?
How might dentinogenesis imperfecta be treated?
How do people inherit dentinogenesis imperfecta?
Researchers have described three types of dentinogenesis imperfecta with similar dental abnormalities. Type I occurs in people who have osteogenesis imperfecta, a genetic condition in which bones are brittle and easily broken. Dentinogenesis imperfecta type II and type III usually occur in people without other inherited disorders. A few families with type II have progressive hearing loss in addition to dental abnormalities. Type III was first identified in a population in Brandywine, Maryland. Some researchers believe that dentinogenesis imperfecta type II and type III, along with a similar condition called dentin dysplasia type II, are actually forms of a single disorder.
Crowns, caps or other forms of dental care are the most commonly used treatments. Dentures or dental implants may be necessary if the majority of teeth are lost.
More detailed information regarding the treatment of dentinogenesis imperfecta can be found by visiting the following web links:
- Dentinogenesis imperfecta. Genetics Home Reference (GHR). November 2009; http://ghr.nlm.nih.gov/condition=dentinogenesisimperfecta. Accessed 4/29/2011.
- Barron MJ, McDonnell ST, MacKie I, Dixon MJ. Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia. Orphanet Journal of Rare Diseases. November 2008; http://www.ojrd.com/content/3/1/31. Accessed 4/29/2011.
- Wulfsberg EA. Dentinogenesis imperfecta. Center for Craniofacial Development and Disorders, Johns Hopkins University. December 29, 2003; http://www.hopkinsmedicine.org/craniofacial/Education/DefinedArticle.cfm?MUArticleID=103&Source=Family. Accessed 5/4/2009.