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Genetic and Rare Diseases Information Center (GARD)

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Dentinogenesis imperfecta 1

Other Names for this Disease
  • Capdepont teeth
  • Dentinogenesis imperfecta Shields type 2
  • Dentinogenesis imperfecta type 1
  • Dentinogenesis imperfecta without osteogenesis imperfecta
  • Opalescent dentin
More Names
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How might dentinogenesis imperfecta be treated?

The aims of treatment are to remove sources of infection or pain, restore aesthetics and protect posterior teeth from wear. Treatment varies according to the age of the patient, severity of the problem and the presenting complaint.[1]

Crowns, caps or other forms of dental care are the most commonly used treatments. Dentures or dental implants may be necessary if the majority of teeth are lost.[2]

More detailed information regarding the treatment of dentinogenesis imperfecta can be found by visiting the following web links:
Last updated: 4/29/2011

  1. Barron MJ, McDonnell ST, MacKie I, Dixon MJ. Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia. Orphanet Journal of Rare Diseases. November 2008; Accessed 4/29/2011.
  2. Wulfsberg EA. Dentinogenesis imperfecta. Center for Craniofacial Development and Disorders, Johns Hopkins University. December 29, 2003; Accessed 5/4/2009.