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Kartagener syndrome

Other Names for this Disease
  • Dextrocardia bronchiectasis and sinusitis
  • Siewert syndrome
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Kartagener syndrome is a type of primary ciliary dyskinesia associated with situs inversus (mirror-image reversal of internal organs).[1] Kartagener syndrome is inherited in an autosomal recessive fashion and is characterized by the triad of situs inversus, bronchiectasis and sinusitis.[2] About 50% of individuals with primary ciliary dyskinesia have Kartagener syndrome.[3]
Last updated: 7/12/2011


  1. Zariwala MA, Knowles MR, Leigh MW. Primary Ciliary Dyskinesia. GeneReviews. October 6, 2009; Accessed 7/12/2011.
  2. Casanova MS, Tuji FM, Yoo HJ, Haiter-Neto F. Kartagener syndrome. Dentomaxillofac Radiol. September 2006; Accessed 7/12/2011.
  3. Primary ciliary dyskinesia. Genetics Home Reference (GHR). August 2010; Accessed 7/12/2011.
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Basic Information

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  • PubMed is a searchable database of medical literature and lists journal articles that discuss Kartagener syndrome. Click on the link to view a sample search on this topic.