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Hemangioma thrombocytopenia syndrome

Other Names for this Disease
  • Kasabach Merritt phenomenon
  • Kasabach Merritt syndrome
  • KMP
  • Thrombocytopenia-hemangioma syndrome
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Hemangioma thrombocytopenia syndrome is characterized by profound thrombocytopenia in association with two rare vascular tumors: kaposiform hemangioendotheliomas and tufted angiomas. The profound thrombocytopenia can cause life threatening bleeding and progress to a disseminated coagulopathy in patients with these tumors.[1][2] The condition typically occurs in early infancy or childhood, although prenatal cases (diagnosed with the aid of ultrasonography), newborn presentations, and rare adult cases have been reported.[3]
Last updated: 10/19/2010


  1. Adams D. Kasabach-Merritt phenomenon. National Organization for Rare Disorders (NORD). 2008; Accessed 10/19/2010.
  2. Vazquez MP. Kasabach-Merritt syndrome. Orphanet. 2006; Accessed 10/19/2010.
  3. Krafchik BR, Hendricks LK, Faguet GB, Kuthiala S. Kasabach-Merritt Syndrome. eMedicine. 2010; Accessed 10/19/2010.
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Basic Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • The Online Mendelian Inheritance in Man (OMIM) is an catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Hemangioma thrombocytopenia syndrome. Click on the link to view a sample search on this topic.