Nevoid basal cell carcinoma syndrome
Other Names for this Disease
- Basal Cell Nevus Syndrome
- Fifth Phacomatosis
- Gorlin Syndrome
- Gorlin-Goltz Syndrome
- Multiple Basal Cell Nevi, Odontogenic Keratocysts, And Skeletal Anomalies
The life expectancy for people with nevoid basal cell carcinoma syndrome (NBCCS) is not significantly different from people without NBCCS. Although young children often have some delay in motor milestones, most of them catch up by about 5 years of age. The major problem is with the cosmetic effect of treatment of multiple skin tumors and treatment of jaw keratocysts. A poor cosmetic outcome can lead to social difficulties, including difficulty maintaining employment.
Last updated: 7/16/2014
- D Gareth Evans and Peter A Farndon. Nevoid Basal Cell Carcinoma Syndrome. GeneReviews. March 7, 2013; http://www.ncbi.nlm.nih.gov/books/NBK1151/. Accessed 7/16/2014.