Other Names for this Disease
- Congenital upward displacement of the scapula
- High scapula
- Maladie de Sprengel familiale
- Sprengel's shoulder
 There may also be anomalies of the bone and soft tissues in the shoulder girdle. The condition is caused by the failure of descent of the shoulder blades during fetal development. It is more common in girls. The condition is most commonly sporadic, although rare familial cases have been reported.Sprengel deformity is a condition where one or both shoulder blades are underdeveloped and abnormally high placed.
Last updated: 5/9/2011
- Sprengel's Deformity. Orthoseek. http://www.orthoseek.com/articles/sprengel.html. Accessed 8/25/2010.
- Ahmad AA. Surgical correction of severe Sprengel deformity to allow greater postoperative range of shoulder abduction. J Pediatr Orthop. 2010 Sep; http://www.ncbi.nlm.nih.gov/pubmed/20733423. Accessed 5/9/2011.
- MM Thacker, Feldman D. Sprengel Deformity. eMedicine. July 6, 2009; http://www.emedicine.com/orthoped/topic445.htm. Accessed 8/25/2010.
- Wawrzynek W, Siemianowicz A, Koczy B, Kasprowska S, Besler K. Usefulness of computed tomography with three-dimensional reconstructions in visualization of cervical spine malformation of a child with Sprengel's deformity. Chir Narzadow Ruchu Orthop Pol. ;. 2005;70(2):131-3; http://www.ncbi.nlm.nih.gov/pubmed/16158872. Accessed 8/25/2010.
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- The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.
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- Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
- PubMed is a searchable database of medical literature and lists journal articles that discuss Sprengel deformity. Click on the link to view a sample search on this topic.