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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Swyer-James syndrome


Other Names for this Disease
  • Swyer-James-MacLeod syndrome
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Treatment


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How might Swyer-James syndrome be treated?

Individuals with Swyer-James syndrome reportedly have been treated conservatively in the past. However, although there are few reports published, it has been recognized that surgical treatment should be considered when infections cannot be controlled. There have been reports of affected individuals being treated with pneumonectomy (removal of a lung), lobectomy (removal of one or more lobes of a lung) or segmentectomy (removal of a specific segment).

It has been proposed that individuals with Swyer-James syndrome may benefit from lung volume reduction surgery (LVRS), a procedure in which damaged tissue is removed from the lung. LVRS was reportedly performed successfully in an individual with Swyer-James syndrome, and it has been suggested that the procedure could be used for managing the condition in other affected individuals because it has shown to be effective for improving pulmonary function and symptoms.[1]
Last updated: 10/21/2011

References
  1. Akira Tasaki, Ryoichi Nakanishi. Lung Volume Reduction Surgery for a Professional Athlete With Swyer-James Syndrome. The Annals of Thoracic Surgery. July 2005; 80(1):342-344.