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Idiopathic pulmonary fibrosis

Other Names for this Disease
  • Familial idiopathic pulmonary fibrosis
  • Fibrocystic pulmonary dysplasia
  • Fibrosing alveolitis
  • Fibrosing alveolitis, cryptogenic
  • Hamman-Rich disease
More Names
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Idiopathic pulmonary fibrosis is a condition in which tissue deep in the lungs becomes thick and stiff, or scarred, over time. As a result the lungs lose their ability to move oxygen to the brain and throughout the body.  Common symptoms include shortness of breath, and dry, hacking cough. “Idiopathic” refers to cases that’s cause is unknown.[1]
Last updated: 12/9/2008


  1. Idiopathic Pulmonary Fibrosis. National Heart, Lung, and Blood Institute (NHLBI). 2007; Accessed 12/9/2008.
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  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • The Online Mendelian Inheritance in Man (OMIM) is an catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Idiopathic pulmonary fibrosis. Click on the link to view a sample search on this topic.

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