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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Primary angiitis of the central nervous system


Other Names for this Disease
  • Granulomatous angiitis of the central nervous system
  • PACNS
  • Primary central nervous system vasculitis
  • Primary CNS vasculitis
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Overview



What is primary angiitis of the central nervous system?


What is primary angiitis of the central nervous system?

Primary angiitis of the central nervous system is a rare form of vasculitis (inflammation of blood vessels) affecting the blood vessels that nourish the brain, spinal cord and peripheral nerves. This condition can lead to narrowing and blockage of the blood vessels of the central nervous system which can eventually cause aneurysms, ischemia and/or hemmorrhage. The cause of this condition is unknown. Signs and symptoms of this condition may begin suddenly or develop over time. Some of the symptoms may incude headaches that do not go away, fever, rapid weight loss, confusion or forgetfulness, and general malaise. Treatment for this condition involves a course of immunosuppresive steroids.[1][2]
Last updated: 10/31/2012

References
  1. Noufal M. Primary Angiitis of the CNS. Medscape Reference. April 2012; http://emedicine.medscape.com/article/1484146-treatment. Accessed 10/29/2012.
  2. NINDS. Vasculitis Syndromes of the Central and Peripheral Nervous Systems Fact Sheet. February 7, 2012; http://www.ninds.nih.gov/disorders/vasculitis/detail_vasculitis.htm. Accessed 10/31/2012.