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Primary angiitis of the central nervous system
Other Names for this Disease
- Granulomatous angiitis of the central nervous system
- Primary central nervous system vasculitis
- Primary CNS vasculitis
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Primary angiitis of the central nervous system is a rare form of vasculitis (inflammation of blood vessels) affecting the blood vessels that nourish the brain, spinal cord and peripheral nerves. This condition can lead to narrowing and blockage of the blood vessels of the central nervous system which can eventually cause aneurysms, ischemia and/or hemmorrhage. The cause of this condition is unknown. Signs and symptoms of this condition may begin suddenly or develop over time. Some of the symptoms may incude headaches that do not go away, fever, rapid weight loss, confusion or forgetfulness, and general malaise. Treatment for this condition involves a course of immunosuppresive steroids.
- Noufal M. Primary Angiitis of the CNS. Medscape Reference. http://emedicine.medscape.com/article/1484146-treatment. Accessed Oct 29, 2012.
- NINDS. Vasculitis Syndromes of the Central and Peripheral Nervous Systems Fact Sheet. http://www.ninds.nih.gov/disorders/vasculitis/detail_vasculitis.htm. Accessed October 31, 2012.
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