Chiari malformation type 1
* Not a rare disease
Other Names for this Disease
- Arnold Chiari malformation type I
- Chiari malformation type I
- Chiari type I malformation
What causes Chiari malformation type 1?
How might Chiari malformation type 1 be treated?
Less frequently, Chiari malformation type 1 is acquired after birth. Causes of acquired Chiari malformation type 1 involve the excessive draining of spinal fluid from the lumbar or thoracic areas of the spine as a result of injury, exposure to harmful substances, or infection. Click here to view a diagram of the spine.
Individuals with more severe symptoms may be in need of surgery. Surgery is the only treatment available to correct functional disturbances or halt the progression of damage to the central nervous system. The goals of surgical treatment are decompression of the point where the skull meets the spine (the cervicomedullary junction) and restoration of normal flow of cerebrospinal fluid in the region of the foramen magnum (the hole in the bottom of the skull where the spinal cord passes to connect to the brain). Prognosis after surgery for the condition is generally good and typically depends on the extent of neurological deficits that were present before the surgery. Most individuals have a reduction of symptoms and/or prolonged periods of relative stability. More than one surgery may be needed to treat the condition.
- Chiari Malformation Fact Sheet. National Institute of Neurological Disorders and Stroke Web site. 2009; http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm. Accessed 12/22/2009.
- Chiari Malformation Fact Sheet. NINDS. February 1, 2012; http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm#194173087. Accessed 3/11/2012.
- Peyman Pakzaban. Chiari Malformation. eMedicine. March 2, 2012; http://emedicine.medscape.com/article/1483583-overview. Accessed 3/11/2012.