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Genetic and Rare Diseases Information Center (GARD)

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Linear porokeratosis

Other Names for this Disease
  • Congenital facial linear porokeratosis (type)
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Linear porokeratosis is a skin condition that most often begins in infancy or early childhood, but it can occur at any age.  The main feature of this condition is the development of reddish brown, slightly raised markings on the skin arranged in lines or streaks on one side of the body.  These markings are not usually painful, though they can sometimes cause open sores in the skin.  There is up to an 11% chance that these markings could progress to skin cancer (basal cell cancer or squamous cell carcinoma) over time.  The exact cause of linear porokeratosis is unknown, but risk factors may include exposure to the sun or radiation, problems with the immune system (immunosuppression), or genetic predisposition.[1]
Last updated: 11/17/2011


  1. Spencer LV . Porokeratosis. Medscape Reference. May 30, 2012; Accessed 8/21/2012.
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Basic Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.

In Depth Information

  • PubMed is a searchable database of medical literature and lists journal articles that discuss Linear porokeratosis. Click on the link to view a sample search on this topic.