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Dermatofibrosarcoma protuberans

Other Names for this Disease
  • DFSP
  • Familial dermatofibrosarcoma protuberans (subtype)
  • Giant cell fibroblastoma
  • Metastatic dermatofibrosarcoma protuberans (subtype)
More Names
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Overview


Dermatofibrosarcoma protuberans is an uncommon tumor that arises in the skin. The tumor is firm and often flesh-colored although it can be reddish, bluish, or purplish. The tumor is often found on the chest or shoulders, but it can be found on other parts of the body.  Dermatofibrosarcoma protuberans may cause no symptoms, and the initial size of the tumor tends to be around 1 to 5 centimeters. This tumor has a low potential to spread to other tissues (metastasize). Treatment often involves surgery to remove the tumor, such as by Mohs’ micrographic surgery. [1]

References

  1. Wood GS. et al. Nonmelanoma Skin Cancers: Basal Cell and Squamous Cell Carcinomas. In: Abeloff et al. Clinical Oncology, 4th ed. Philadelphia, PA: Churchill Livingstone; 2008.
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General Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition. Click on the link to view the information.
  • Genetics Home Reference (GHR) contains information on Dermatofibrosarcoma protuberans. Click on the link to go to GHR and review the information.
  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • MeSH® (Medical Subject Headings) is a terminology tool used by the National Library of Medicine. Click on the link to view information on this topic.
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.  Click on the link to read information on this topic.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Dermatofibrosarcoma protuberans. Click on the link to view a sample search on this topic.
  • The The Online Mendelian Inheritance in Man (OMIM) database contains genetics resources that discuss Dermatofibrosarcoma protuberans. Click on the link to go to OMIM and review these resources.