{"Name":"Lichen planus pigmentosus","DiseaseID__c":"GARD:0010816","id":10816,"encodedName":"lichen-planus-pigmentosus","IsDeleted":false,"Disease_Name_Full__c":"Lichen planus pigmentosus","Xref_IDs__c":"717061002; C0406366; MEDGEN:590349; MONDO:0016774; ORPHA:254463","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":1,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":4,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0016774","Disease_Description__c":"Lichen planus (LP) pigmentosus is a rare variant of cutaneous lichen planus (see this term) characterized by the presence of hyperpigmented lichenoid lesions in sun-exposed or flexural areas of the body.","GARD_Name__c":"Lichen planus pigmentosus","GARD_Synonym__c":"lichen planus pigmentosa; lichen planus pigmentosus inversus; lp pigmentosa; lp pigmentosus; post-inflammatory hyperpigmentation in lichen planus","Curated_Disease_Description_Source__c":"GARD:0010816","Curated_Disease_Description__c":"Lichen planus pigmentosus (LPP) is a rare form of lichen planus. It is characterized by oval or irregularly-shaped brown to gray-brown macules and patches on the skin. Areas that are exposed to sun such as the forehead, temples and neck are most commonly affected. However, the macules and patches may also develop on the trunk or in places where two areas of skin touch or rub together (i.e. the armpit, groin, etc). The cause of LPP is unknown, but studies suggest it may be triggered by UV light, viral infections, or agents applied to the skin such as mustard oil and amla oil.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":"as an Adult","SourceID__c":"ORPHA:254463","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0016774","ORPHANET_ID__c":"ORPHA:254463","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Liquen plano pigmentoso","Spanish_Description_Source__c":"ORPHA:254463","Spanish_Description__c":"El liquen plano (LP) pigmentoso es una variante rara del liquen plano cutáneo (consulte este término) caracterizado por la presencia de lesiones liquenoides hiperpigmentadas en áreas del cuerpo expuestas al sol o de flexión.","Spanish_Disease_Name__c":"liquen plano pigmentoso","Spanish_GARD_Synonym__c":"liquen plano pigmentoso inverso; lp pigmentosa; lp pigmentoso","Category_Linearization__c":"ORPHA:89826","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Lichen planus pigmentosus (LPP) is a rare form of lichen planus. It is characterized by oval or irregularly-shaped brown to gray-brown macules and patches on the skin. Areas that are exposed to sun such as the forehead, temples and neck are most commonly affected. However, the macules and patches may also develop on the trunk or in places where two areas of skin touch or rub together (i.e. the armpit, groin, etc). The cause of LPP is unknown, but studies suggest it may be triggered by UV light, viral infections, or agents applied to the skin such as mustard oil and amla oil.","Curated_Disease_Description_Source__c":"GARD:0010816","GARD_Synonym__c":"lichen planus pigmentosa; lichen planus pigmentosus inversus; lp pigmentosa; lp pigmentosus; post-inflammatory hyperpigmentation in lichen planus","Name":"Lichen planus pigmentosus","estimateUsa":""}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Alianza Iberoamericana de Enfermedades Raras o Poco Frecuentes","Website__c":"https://aliber.org/web/"},{"Account_Name__c":"Federación Mexicana de Enfermedades Raras (FEMEXER)","Website__c":"http://www.femexer.org/"},{"Account_Name__c":"Federación Española de Enfermedades Raras","Website__c":"https://enfermedades-raras.org/"},{"Account_Name__c":"Federación Colombiana de Enfermedades Raras","Website__c":"http://www.fecoer.org"},{"Account_Name__c":"Federación Argentina de Enfermedades Poco Frecuentes","Website__c":"https://fadepof.org.ar/"},{"Account_Name__c":"Asociación Todos Unidos Enfermedades Raras Uruguay","Website__c":"https://atueru.org.uy/"},{"Account_Name__c":"American Skin Association","Website__c":"https://www.americanskin.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"Adult","Provided_By__c":"ORPHA:254463"}],"External_Identifier_Disease__c":[{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=717061002","Source__c":"C0406366; MONDO:0016774","Xref__c":"717061002"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0406366","Source__c":"C0406366","Xref__c":"C0406366"},{"URL__c":"https://www.orpha.net/en/disease/detail/254463","Source__c":"C0406366; MONDO:0016774; ORPHA:254463","Xref__c":"ORPHA:254463"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=590349","Source__c":"C0406366","Xref__c":"MEDGEN:590349"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=238649008","Source__c":"C0406366","Xref__c":"238649008"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0016774","Source__c":"GARD:0010816","Xref__c":"MONDO:0016774"}],"tags":{"Account":["Dermatology"],"Disease Category":["Dermatology"],"Specialist":["Dermatology"]},"synonyms":["lichen planus pigmentosa"," lichen planus pigmentosus inversus"," lp pigmentosa"," lp pigmentosus"," post-inflammatory hyperpigmentation in lichen planus"],"spanishId":12329,"spanishName":"liquen-plano-pigmentoso"}