{"Name":"Frontal fibrosing alopecia","DiseaseID__c":"GARD:0010886","id":10886,"encodedName":"frontal-fibrosing-alopecia","IsDeleted":false,"Disease_Name_Full__c":"Frontal fibrosing alopecia","Xref_IDs__c":"717055000; C4255374; MEDGEN:899012; MONDO:0016776; ORPHA:254492","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":1,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":5,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0016776","Disease_Description__c":"Frontal fibrosing alopecia (FFA) is a rare variant of lichen planopilaris (see this term) characterized by symmetrical, progressive, band-like anterior hair loss of the scalp.","GARD_Name__c":"Frontal fibrosing alopecia","GARD_Synonym__c":"ffa","Curated_Disease_Description_Source__c":"GARD:0010886","Curated_Disease_Description__c":"Frontal fibrosing alopecia (FFA) is a form of lichen planopilaris that is characterized primarily by slowly progressive hair loss (alopecia) and scarring on the scalp near the forehead. In some cases, the eyebrows, eye lashes and/or other parts of the body may be involved, as well. Although it has been suggested that FFA may be due to hormonal changes or an autoimmune response, the exact cause of this condition is not yet known.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":"as an Adult","SourceID__c":"ORPHA:254492","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0016776","ORPHANET_ID__c":"ORPHA:254492","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Alopecia frontal fibrosante","Spanish_Description_Source__c":"ORPHA:254492","Spanish_Description__c":"La alopecia frontal fibrosante (FFA) es una variante poco frecuente del liquen plano pilar (consulte este término) que se caracteriza por una pérdida progresiva simétrica en forma de banda del pelo del cuero cabelludo.","Spanish_Disease_Name__c":"alopecia frontal fibrosante","Spanish_GARD_Synonym__c":"ffa","Category_Linearization__c":"ORPHA:89826","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Frontal fibrosing alopecia (FFA) is a form of lichen planopilaris that is characterized primarily by slowly progressive hair loss (alopecia) and scarring on the scalp near the forehead. In some cases, the eyebrows, eye lashes and/or other parts of the body may be involved, as well. Although it has been suggested that FFA may be due to hormonal changes or an autoimmune response, the exact cause of this condition is not yet known.","Curated_Disease_Description_Source__c":"GARD:0010886","GARD_Synonym__c":"ffa","Name":"Frontal fibrosing alopecia","estimateUsa":""}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Scarring Alopecia Foundation","Website__c":"https://scarringalopecia.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"Adult","Provided_By__c":"ORPHA:254492"}],"External_Identifier_Disease__c":[{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=717055000","Source__c":"C4255374; MONDO:0016776","Xref__c":"717055000"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=899012","Source__c":"C4255374","Xref__c":"MEDGEN:899012"},{"URL__c":"https://www.orpha.net/en/disease/detail/254492","Source__c":"C4255374; MONDO:0016776; ORPHA:254492","Xref__c":"ORPHA:254492"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C4255374","Source__c":"C4255374","Xref__c":"C4255374"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0016776","Source__c":"GARD:0010886","Xref__c":"MONDO:0016776"}],"tags":{"Account":["Dermatology"],"Disease Category":["Dermatology"],"Specialist":["Dermatology"]},"synonyms":["ffa"]}