{"Name":"La Crosse encephalitis","DiseaseID__c":"GARD:0010925","id":10925,"encodedName":"la-crosse-encephalitis","IsDeleted":false,"Disease_Name_Full__c":"La Crosse encephalitis","Xref_IDs__c":"61094002; C0276379; D004670; DOID:0050118; MEDGEN:547309; MONDO:0019378; ORPHA:83483","USA_Estimate__c":"50,000","No_of_Specialist_Tagsa__c":4,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":"80,000 to 800,000","No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":5,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0019378","Disease_Description__c":"An acute arboviral infection caused by the <i>La Crosse bunyavirus</i> transmitted by an infected mosquito, usually observed in infants, children or adolescents (6 months to 16 years), and characterized by the onset of flulike symptoms such as fever, chills, nausea, vomiting, headache, and abdominal pain, followed by the onset of encephalitis characterized by somnolence, obtundation, and even seizures, focal neurologic signs (asymmetrical reflexes or Babinski signs), paralysis or even coma. CE can leave sequelae such as residual epilepsy and neurocognitive deficits.","GARD_Name__c":"La Crosse encephalitis","GARD_Synonym__c":"california encephalitis; california virus encephalitis; californian encephalitis; la crosse virus caused infectious encephalitis; la crosse virus encephalitis; la crosse virus infectious encephalitis; lac - la crosse encephalitis; neuroinvasive california encephalitis virus infection","Curated_Disease_Description_Source__c":"GARD:0010925","Curated_Disease_Description__c":"La Crosse (LAC) encephalitis is a mosquito-borne virus that was first described in La Crosse, Wisconsin in 1963. Since then, it has been reported in several Midwestern and Mid-Atlantic states. The LAC virus is one of many mosquito-transmitted viruses that can cause an inflammation of the brain (encephalitis). About 80-100 cases of this condition are reported each year in the United States. Most cases occur in children younger than age 16. While most people who become infected have no symptoms, those who do become ill may have fever, headache, vomiting and lethargy (tiredness). Severe cases develop encephalitis accompanied by seizures. Coma and paralysis occur in some cases.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":"50,000","Age_at_Onset_Snippet_Text__c":"at any time in life","SourceID__c":"ORPHA:83483","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0019378","ORPHANET_ID__c":"ORPHA:83483","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Encefalitis de la crosse","Spanish_Description_Source__c":"ORPHA:83483","Spanish_Description__c":"Es una infección arboviral aguda causada por el virus de La Crosse, perteneciente a la familia <i>Bunyaviridae</i>, transmitida por un mosquito infectado y, generalmente descrita en lactantes, niños o adolescentes (de 6 meses a 16 años de edad). Está caracterizada por un inicio de síntomas similares a la gripe, tales como fiebre, escalofríos, náuseas, vómitos, cefalea y dolor abdominal, seguidos por la aparición de encefalitis que se manifiesta como somnolencia, obnubilación y posibles crisis epilépticas, signos neurológicos focales (reflejos asimétricos o signo de Babinski), parálisis e incluso coma. La infección puede dejar secuelas tales como epilepsias residuales y déficits neurocognitivos.","Spanish_Disease_Name__c":"encefalitis de la crosse","Spanish_GARD_Synonym__c":"encefalitis californiana","Category_Linearization__c":"ORPHA:68416","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"La Crosse (LAC) encephalitis is a mosquito-borne virus that was first described in La Crosse, Wisconsin in 1963. Since then, it has been reported in several Midwestern and Mid-Atlantic states. The LAC virus is one of many mosquito-transmitted viruses that can cause an inflammation of the brain (encephalitis). About 80-100 cases of this condition are reported each year in the United States. Most cases occur in children younger than age 16. While most people who become infected have no symptoms, those who do become ill may have fever, headache, vomiting and lethargy (tiredness). Severe cases develop encephalitis accompanied by seizures. Coma and paralysis occur in some cases.","Curated_Disease_Description_Source__c":"GARD:0010925","GARD_Synonym__c":"california encephalitis; california virus encephalitis; californian encephalitis; la crosse virus caused infectious encephalitis; la crosse virus encephalitis; la crosse virus infectious encephalitis; lac - la crosse encephalitis; neuroinvasive california encephalitis virus infection","Name":"La Crosse encephalitis","Curated_USA_Estimate__c":"50,000","estimateUsa":"50,000"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Infectious Disease","Tag_Category__c":"Disease Category;Specialist","category_description":"Infectious diseases are caused by bacteria, viruses, fungi, or parasites entering the body, multiplying, and spreading illness.","curated_tag_name":"Infectious diseases"},{"Tag_Name__c":"Neurology","Tag_Category__c":"Disease Category;Specialist","category_description":"Neurological diseases affect the brain, spinal cord, cranial nerves, autonomic nerves, or other peripheral nerves.","curated_tag_name":"Neurological diseases"},{"Tag_Name__c":"Rare Viral Disease","Tag_Category__c":"Cause","curated_tag_name":"Viral Infectious Diseases"},{"Tag_Name__c":"Epilepsy","Tag_Category__c":"Account;Specialist","curated_tag_name":"Epilepsy"},{"Tag_Name__c":"Pediatrics","Tag_Category__c":"Specialist"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"All ages","Provided_By__c":"ORPHA:83483"}],"External_Identifier_Disease__c":[{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=61094002","Source__c":"C0276379; MONDO:0019378","Xref__c":"61094002"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0276379","Source__c":"C0276379","Xref__c":"C0276379"},{"URL__c":"https://www.orpha.net/en/disease/detail/83483","Source__c":"C0276379; MONDO:0019378; ORPHA:83483","Xref__c":"ORPHA:83483"},{"URL__c":"https://www.ebi.ac.uk/ols4/ontologies/doid/classes?obo_id=DOID%3A0050118","Source__c":"MONDO:0019378","Xref__c":"DOID:0050118"},{"URL__c":"https://www.ncbi.nlm.nih.gov/mesh/C004670","Source__c":"MONDO:0019378","Xref__c":"D004670"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=547309","Source__c":"C0276379","Xref__c":"MEDGEN:547309"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0019378","Source__c":"GARD:0010925","Xref__c":"MONDO:0019378"}],"tags":{"Disease Category":["Infectious Disease","Neurology"],"Specialist":["Infectious Disease","Neurology","Epilepsy","Pediatrics"],"Cause":["Rare Viral Disease"],"Account":["Epilepsy"]},"synonyms":["california encephalitis"," california virus encephalitis"," californian encephalitis"," la crosse virus caused infectious encephalitis"," la crosse virus encephalitis"," la crosse virus infectious encephalitis"," lac - la crosse encephalitis"," neuroinvasive california encephalitis virus infection"]}