{"Name":"Linear lichen planus","DiseaseID__c":"GARD:0011898","id":11898,"encodedName":"linear-lichen-planus","IsDeleted":false,"Disease_Name_Full__c":"Linear lichen planus","Xref_IDs__c":"44509000; C0023650; MEDGEN:507921; MONDO:0016769; ORPHA:254379","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":2,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":2,"Disease_Characteristics_Score__c":5,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0016769","Disease_Description__c":"Linear lichen planus (LLP), also referred to as Blaschkoid LP, is a rare type of lichen planus characterized by a linear distribution of lichenoid lesions along the lines of Blaschko, which are embryonic pathways of skin development.","GARD_Name__c":"Linear lichen planus","GARD_Synonym__c":"blaschkoid lichen planus; blaschkoid lp; lichen planus linearis; linear lp","Curated_Disease_Description_Source__c":"GARD:0011898","Curated_Disease_Description__c":"Linear lichen planus (LLP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In LLP, specifically, affected people develop itchy, purple, flat-topped papules (bumps) in a linear distribution along the lines of Blaschko. Although these papules can be found anywhere on the body, they most commonly affect the limbs (arms and legs). The exact underlying cause of LLP is unknown; however, it has been associated with metastatic cancer, HIV infection and hepatitis C infection.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":"at any time in life","SourceID__c":"ORPHA:254379","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0016769","ORPHANET_ID__c":"ORPHA:254379","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Liquen plano lineal","Spanish_Description_Source__c":"ORPHA:254379","Spanish_Description__c":"El liquen plano lineal (LPL), también denominado LP blaschkoide, es una variante poco frecuente de liquen plano caracterizado por una distribución lineal de lesiones liquenoides siguiendo las líneas de Blaschko, que reflejan el patrón de migración celular cutáneo durante el desarrollo embrionario.","Spanish_Disease_Name__c":"liquen plano lineal","Spanish_GARD_Synonym__c":"liquen plano blaschkoide; lp blaschkoide; lp linear","Category_Linearization__c":"ORPHA:89826","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Linear lichen planus (LLP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In LLP, specifically, affected people develop itchy, purple, flat-topped papules (bumps) in a linear distribution along the lines of Blaschko. Although these papules can be found anywhere on the body, they most commonly affect the limbs (arms and legs). The exact underlying cause of LLP is unknown; however, it has been associated with metastatic cancer, HIV infection and hepatitis C infection.","Curated_Disease_Description_Source__c":"GARD:0011898","GARD_Synonym__c":"blaschkoid lichen planus; blaschkoid lp; lichen planus linearis; linear lp","Name":"Linear lichen planus","estimateUsa":""}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Autoimmune Association","Website__c":"https://autoimmune.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"},{"Tag_Name__c":"Pediatrics","Tag_Category__c":"Specialist"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"All ages","Provided_By__c":"ORPHA:254379"}],"External_Identifier_Disease__c":[{"URL__c":"https://www.orpha.net/en/disease/detail/254379","Source__c":"C0023650; MONDO:0016769; ORPHA:254379","Xref__c":"ORPHA:254379"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0023650","Source__c":"C0023650","Xref__c":"C0023650"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=507921","Source__c":"C0023650","Xref__c":"MEDGEN:507921"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=44509000","Source__c":"C0023650; MONDO:0016769","Xref__c":"44509000"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0016769","Source__c":"GARD:0011898","Xref__c":"MONDO:0016769"}],"tags":{"Account":["Dermatology"],"Disease Category":["Dermatology"],"Specialist":["Dermatology","Pediatrics"]},"synonyms":["blaschkoid lichen planus"," blaschkoid lp"," lichen planus linearis"," linear lp"]}