{"Name":"Angioimmunoblastic T-cell lymphoma","DiseaseID__c":"GARD:0011973","id":11973,"encodedName":"angioimmunoblastic-t-cell-lymphoma","IsDeleted":false,"Disease_Name_Full__c":"Angioimmunoblastic T-cell lymphoma","Xref_IDs__c":"413537009; 423022357; 835009; C0020981; C7528; C86.5; D007119; DOID:0111147; MEDGEN:7025; MONDO:0004977; ORPHA:86886","USA_Estimate__c":"1,000","No_of_Specialist_Tagsa__c":2,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":1,"World_Estimate__c":"1 to 8,000","No_of_HRSA_records__c":0,"Evidence_Based_Score__c":1,"No_of_Disease_Descriptions__c":2,"Disease_Characteristics_Score__c":4,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0004977","Disease_Description__c":"A mature T-cell non-Hodgkin lymphoma, characterized by systemic disease and a polymorphous infiltrate involving lymph nodes and extranodal sites. The clinical course is typically aggressive.","GARD_Name__c":"Angioimmunoblastic T-cell lymphoma","GARD_Synonym__c":"aild; ailt; angioimmunoblastic lymphadenopathy; angioimmunoblastic lymphadenopathy type t-cell lymphoma; angioimmunoblastic lymphadenopathy with dysproteinemia; angioimmunoblastic lymphoma; immunoblastic lymphadenopathy; lymphogranulomatosis x; peripheral t-cell lymphoma, aild (angioimmunoblastic lymphadenopathy with dysproteinemia); t-cell lymphoma, aild type","Curated_Disease_Description_Source__c":"MONDO:0004977","Curated_Disease_Description__c":"A mature T-cell non-Hodgkin lymphoma, characterized by systemic disease and a polymorphous infiltrate involving lymph nodes and extranodal sites. The clinical course is typically aggressive.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":"1,000","Age_at_Onset_Snippet_Text__c":"as an Adult","SourceID__c":"ORPHA:86886","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0004977","ORPHANET_ID__c":"ORPHA:86886","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Linfoma angioinmunoblástico de células t","Spanish_Description_Source__c":null,"Spanish_Description__c":null,"Spanish_Disease_Name__c":"linfoma angioinmunoblástico de células t","Spanish_GARD_Synonym__c":"linfoma de células t tipo aild","Category_Linearization__c":"ORPHA:250908","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"A mature T-cell non-Hodgkin lymphoma, characterized by systemic disease and a polymorphous infiltrate involving lymph nodes and extranodal sites. The clinical course is typically aggressive.","Curated_Disease_Description_Source__c":"MONDO:0004977","GARD_Synonym__c":"aild; ailt; angioimmunoblastic lymphadenopathy; angioimmunoblastic lymphadenopathy type t-cell lymphoma; angioimmunoblastic lymphadenopathy with dysproteinemia; angioimmunoblastic lymphoma; immunoblastic lymphadenopathy; lymphogranulomatosis x; peripheral t-cell lymphoma, aild (angioimmunoblastic lymphadenopathy with dysproteinemia); t-cell lymphoma, aild type","Name":"Angioimmunoblastic T-cell lymphoma","Curated_USA_Estimate__c":"1,000","estimateUsa":"1,000"}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Lymphoma Research Foundation","Website__c":"https://lymphoma.org/"},{"Account_Name__c":"HealthTree Foundation","Website__c":"https://healthtree.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Cancer - Oncologist","Tag_Category__c":"Specialist"},{"Tag_Name__c":"Cancer","Tag_Category__c":"Disease Category","category_description":"Cancer is a disease in which some of the body's cells grow uncontrollably and can spread to other parts of the body.","curated_tag_name":"Cancer"},{"Tag_Name__c":"Hematology","Tag_Category__c":"Disease Category;Specialist","category_description":"Blood diseases affect the blood or blood-forming organs, including red blood cells, white blood cells, platelets, plasma, and bone marrow.","curated_tag_name":"Blood diseases"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"Adult","Provided_By__c":"ORPHA:86886"}],"External_Identifier_Disease__c":[{"URL__c":"http://purl.bioontology.org/ontology/ICD10CM/C86.5","Source__c":"MONDO:0004977","Xref__c":"C86.5"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=413537009","Source__c":"C0020981; MONDO:0004977","Xref__c":"413537009"},{"URL__c":"https://evsexplore.semantics.cancer.gov/evsexplore/concept/ncit/C7528","Source__c":"C0020981; MONDO:0004977","Xref__c":"C7528"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=7025","Source__c":"C0020981","Xref__c":"MEDGEN:7025"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0020981","Source__c":"C0020981","Xref__c":"C0020981"},{"URL__c":"https://www.orpha.net/en/disease/detail/86886","Source__c":"C0020981; MONDO:0004977; ORPHA:86886","Xref__c":"ORPHA:86886"},{"URL__c":"https://www.ebi.ac.uk/ols4/ontologies/doid/classes?obo_id=DOID%3A0111147","Source__c":"MONDO:0004977","Xref__c":"DOID:0111147"},{"URL__c":"https://www.ncbi.nlm.nih.gov/mesh/C007119","Source__c":"C0020981; MONDO:0004977","Xref__c":"D007119"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=52097008","Source__c":"C0020981","Xref__c":"52097008"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0004977","Source__c":"GARD:0011973","Xref__c":"MONDO:0004977"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=835009","Source__c":"C0020981","Xref__c":"835009"},{"URL__c":"https://secure.ssa.gov/apps10/poms.nsf/lnx/0423022357","Xref__c":"423022357"}],"tags":{"Specialist":["Cancer - Oncologist","Hematology"],"Disease Category":["Cancer","Hematology"]},"synonyms":["aild"," ailt"," angioimmunoblastic lymphadenopathy"," angioimmunoblastic lymphadenopathy type t-cell lymphoma"," angioimmunoblastic lymphadenopathy with dysproteinemia"," angioimmunoblastic lymphoma"," immunoblastic lymphadenopathy"," lymphogranulomatosis x"," peripheral t-cell lymphoma, aild (angioimmunoblastic lymphadenopathy with dysproteinemia)"," t-cell lymphoma, aild type"]}