{"Name":"Atrophic lichen planus","DiseaseID__c":"GARD:0012675","id":12675,"encodedName":"atrophic-lichen-planus","IsDeleted":false,"Disease_Name_Full__c":"Atrophic lichen planus","Xref_IDs__c":"25858008; C0023647; C34777; MEDGEN:9754; MONDO:0016773; ORPHA:254449","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":2,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":5,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0016773","Disease_Description__c":"A rare variant of cutaneous lichen planus characterized by the development of pale papules or plaques with an atrophic center.","GARD_Name__c":"Atrophic lichen planus","GARD_Synonym__c":"atrophic lp; lichen planus atrophicus","Curated_Disease_Description_Source__c":"GARD:0012675","Curated_Disease_Description__c":"Atrophic lichen planus (LP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In atrophic LP, specifically, affected people develop pale papules or plaques with an atrophic (broken down tissue) center. Although these papules can be found anywhere on the body, they most commonly affect the trunk and/or legs on skin areas previously affected by classic lichen planus. The exact underlying cause of atrophic LP is unknown.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":"at any time in life","SourceID__c":"ORPHA:254449","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0016773","ORPHANET_ID__c":"ORPHA:254449","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Liquen plano atrófico","Spanish_Description_Source__c":"ORPHA:254449","Spanish_Description__c":"Es una variante poco frecuente del liquen plano cutáneo caracterizado por el desarrollo de pápulas pálidas o placas con atrofia central.","Spanish_Disease_Name__c":"liquen plano atrófico","Spanish_GARD_Synonym__c":null,"Category_Linearization__c":"ORPHA:89826","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Atrophic lichen planus (LP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In atrophic LP, specifically, affected people develop pale papules or plaques with an atrophic (broken down tissue) center. Although these papules can be found anywhere on the body, they most commonly affect the trunk and/or legs on skin areas previously affected by classic lichen planus. The exact underlying cause of atrophic LP is unknown.","Curated_Disease_Description_Source__c":"GARD:0012675","GARD_Synonym__c":"atrophic lp; lichen planus atrophicus","Name":"Atrophic lichen planus","estimateUsa":""}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Autoimmune Association","Website__c":"https://autoimmune.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"},{"Tag_Name__c":"Pediatrics","Tag_Category__c":"Specialist"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"All ages","Provided_By__c":"ORPHA:254449"}],"External_Identifier_Disease__c":[{"URL__c":"https://evsexplore.semantics.cancer.gov/evsexplore/concept/ncit/C34777","Source__c":"C0023647; MONDO:0016773","Xref__c":"C34777"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=9754","Source__c":"C0023647","Xref__c":"MEDGEN:9754"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0023647","Source__c":"C0023647","Xref__c":"C0023647"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=25858008","Source__c":"C0023647; MONDO:0016773","Xref__c":"25858008"},{"URL__c":"https://www.orpha.net/en/disease/detail/254449","Source__c":"C0023647; MONDO:0016773; ORPHA:254449","Xref__c":"ORPHA:254449"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0016773","Source__c":"GARD:0012675","Xref__c":"MONDO:0016773"}],"tags":{"Account":["Dermatology"],"Disease Category":["Dermatology"],"Specialist":["Dermatology","Pediatrics"]},"synonyms":["atrophic lp"," lichen planus atrophicus"]}