{"Name":"Annular atrophic lichen planus","DiseaseID__c":"GARD:0012676","id":12676,"encodedName":"annular-atrophic-lichen-planus","IsDeleted":false,"Disease_Name_Full__c":"Annular atrophic lichen planus","Xref_IDs__c":"720493003; C4304037; MEDGEN:929706; MONDO:0016771; ORPHA:254411","USA_Estimate__c":"1,000","No_of_Specialist_Tagsa__c":1,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":"1 to 8,000","No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":4,"Disease_Characteristics_Score__c":5,"No_of_Age_at_Onset__c":1,"Description_Source__c":"MONDO:0016771","Disease_Description__c":"A rare variant of cutaneous lichen planus characterized by both annular and atrophic LP features in the same lesion.","GARD_Name__c":"Annular atrophic lichen planus","GARD_Synonym__c":"annular atrophic lp","Curated_Disease_Description_Source__c":"GARD:0012676","Curated_Disease_Description__c":"Annular atrophic lichen planus (LP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In annular atrophic LP, specifically, affected people develop skin lesions with features of both annular LP and atrophic LP - ring-shaped, slightly raised, purple lesions with central atrophy (tissue breakdown). Although these lesions can be found anywhere on the body, they most commonly affect the trunk and legs. The exact underlying cause of annular atrophic LP is unknown.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":"1,000","Age_at_Onset_Snippet_Text__c":"as an Adult","SourceID__c":"ORPHA:254411","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0016771","ORPHANET_ID__c":"ORPHA:254411","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Liquen plano anular atrófico","Spanish_Description_Source__c":"ORPHA:254411","Spanish_Description__c":"Es una variante poco frecuente del liquen plano (LP) cutáneo caracterizada por rasgos de LP anular y atrófico en una misma lesión.","Spanish_Disease_Name__c":"liquen plano anular atrófico","Spanish_GARD_Synonym__c":null,"Category_Linearization__c":"ORPHA:89826","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Annular atrophic lichen planus (LP) is a rare form of lichen planus, which is a condition that affects the skin and/or mouth. In annular atrophic LP, specifically, affected people develop skin lesions with features of both annular LP and atrophic LP - ring-shaped, slightly raised, purple lesions with central atrophy (tissue breakdown). Although these lesions can be found anywhere on the body, they most commonly affect the trunk and legs. The exact underlying cause of annular atrophic LP is unknown.","Curated_Disease_Description_Source__c":"GARD:0012676","GARD_Synonym__c":"annular atrophic lp","Name":"Annular atrophic lichen planus","Curated_USA_Estimate__c":"1,000","estimateUsa":"1,000"}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Autoimmune Association","Website__c":"https://autoimmune.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"}],"Age_At_Onset__c":[{"Age_At_Onset__c":"Adult","Provided_By__c":"ORPHA:254411"}],"External_Identifier_Disease__c":[{"URL__c":"https://www.orpha.net/en/disease/detail/254411","Source__c":"C4304037; MONDO:0016771; ORPHA:254411","Xref__c":"ORPHA:254411"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C4304037","Source__c":"C4304037","Xref__c":"C4304037"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=929706","Source__c":"C4304037","Xref__c":"MEDGEN:929706"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=720493003","Source__c":"C4304037; MONDO:0016771","Xref__c":"720493003"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0016771","Source__c":"GARD:0012676","Xref__c":"MONDO:0016771"}],"tags":{"Account":["Dermatology"],"Disease Category":["Dermatology"],"Specialist":["Dermatology"]},"synonyms":["annular atrophic lp"]}