{"Name":"Primary cutaneous follicle center lymphoma","DiseaseID__c":"GARD:0013701","id":13701,"encodedName":"primary-cutaneous-follicle-center-lymphoma","IsDeleted":false,"Disease_Name_Full__c":"Primary cutaneous follicle center lymphoma","Xref_IDs__c":"404143002; C1333171; C7217; C82.6; MEDGEN:234180; MONDO:0015814; ORPHA:178540","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":3,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":4,"No_of_Age_at_Onset__c":0,"Description_Source__c":"MONDO:0015814","Disease_Description__c":"A primary lymphoma of the skin composed of various numbers of small and large irregular neoplastic follicle center cells. Its morphologic pattern can be nodular, diffuse, or nodular and diffuse. It presents with solitary or grouped plaques and tumors, and it usually involves the scalp, forehead, or trunk. It rarely involves the legs. This type of cutaneous lymphoma tends to remain localized to the skin.","GARD_Name__c":"Primary cutaneous follicle center lymphoma","GARD_Synonym__c":"crosti's disease; crosti's lymphoma; cutaneous follicle center lymphoma; cutaneous follicle centre lymphoma; pcfcl; primary cutaneous follicle center cell lymphoma; primary cutaneous follicular center b-cell lymphoma; reticulohistiocytoma of the dorsum","Curated_Disease_Description_Source__c":"PlainLanguagePilotV1-Sep23","Curated_Disease_Description__c":"Primary cutaneous follicle center lymphoma is a rare slow-growing type of skin cancer that develops from B cells. It is characterized by a solitary or group of red patches or lumps (erythematous plaques or tumors) usually on the head, neck, or trunk. When found in groups, they can grow based on the hair follicles of the region, randomly, or a mix of both. The patches are smooth and do not usually break open.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":null,"SourceID__c":"ORPHA:178540","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0015814","ORPHANET_ID__c":"ORPHA:178540","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Linfoma cutáneo primario del centro folicular","Spanish_Description_Source__c":null,"Spanish_Description__c":null,"Spanish_Disease_Name__c":"linfoma cutáneo primario del centro folicular","Spanish_GARD_Synonym__c":"pcfcl","Category_Linearization__c":"ORPHA:250908","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Primary cutaneous follicle center lymphoma is a rare slow-growing type of skin cancer that develops from B cells. It is characterized by a solitary or group of red patches or lumps (erythematous plaques or tumors) usually on the head, neck, or trunk. When found in groups, they can grow based on the hair follicles of the region, randomly, or a mix of both. The patches are smooth and do not usually break open.","Curated_Disease_Description_Source__c":"PlainLanguagePilotV1-Sep23","GARD_Synonym__c":"crosti's disease; crosti's lymphoma; cutaneous follicle center lymphoma; cutaneous follicle centre lymphoma; pcfcl; primary cutaneous follicle center cell lymphoma; primary cutaneous follicular center b-cell lymphoma; reticulohistiocytoma of the dorsum","Name":"Primary cutaneous follicle center lymphoma","estimateUsa":""}],"Organization_Supported_Diseases__c":[{"Account_Name__c":"Lymphoma Research Foundation","Website__c":"https://lymphoma.org/"}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Cancer - Oncologist","Tag_Category__c":"Specialist"},{"Tag_Name__c":"Cancer","Tag_Category__c":"Disease Category","category_description":"Cancer is a disease in which some of the body's cells grow uncontrollably and can spread to other parts of the body.","curated_tag_name":"Cancer"},{"Tag_Name__c":"Dermatology","Tag_Category__c":"Account;Disease Category;Specialist","category_description":"Skin diseases, or integumentary system diseases, affect the skin, hair, nails, sweat glands, or oil glands.","curated_tag_name":"Skin diseases"},{"Tag_Name__c":"Hematology","Tag_Category__c":"Disease Category;Specialist","category_description":"Blood diseases affect the blood or blood-forming organs, including red blood cells, white blood cells, platelets, plasma, and bone marrow.","curated_tag_name":"Blood diseases"}],"External_Identifier_Disease__c":[{"URL__c":"https://www.orpha.net/en/disease/detail/178540","Source__c":"C1333171; MONDO:0015814; ORPHA:178540","Xref__c":"ORPHA:178540"},{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C1333171","Source__c":"C1333171","Xref__c":"C1333171"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=404143002","Source__c":"C1333171; MONDO:0015814","Xref__c":"404143002"},{"URL__c":"https://evsexplore.semantics.cancer.gov/evsexplore/concept/ncit/C7217","Source__c":"C1333171; MONDO:0015814","Xref__c":"C7217"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=234180","Source__c":"C1333171","Xref__c":"MEDGEN:234180"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=419662008","Source__c":"C1333171","Xref__c":"419662008"},{"URL__c":"http://purl.bioontology.org/ontology/ICD10CM/C82.6","Source__c":"MONDO:0015814","Xref__c":"C82.6"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0015814","Source__c":"GARD:0013701","Xref__c":"MONDO:0015814"}],"tags":{"Specialist":["Cancer - Oncologist","Dermatology","Hematology"],"Disease Category":["Cancer","Dermatology","Hematology"],"Account":["Dermatology"]},"synonyms":["crosti's disease"," crosti's lymphoma"," cutaneous follicle center lymphoma"," cutaneous follicle centre lymphoma"," pcfcl"," primary cutaneous follicle center cell lymphoma"," primary cutaneous follicular center b-cell lymphoma"," reticulohistiocytoma of the dorsum"]}