{"Name":"Kluver-Bucy syndrome","DiseaseID__c":"GARD:0006840","id":6840,"encodedName":"kluver-bucy-syndrome","IsDeleted":false,"Disease_Name_Full__c":"Kluver-Bucy syndrome","Xref_IDs__c":"10651001; C0270707; C84802; D020232; DOID:2510; MEDGEN:124361; MONDO:0005817; ORPHA:157823","USA_Estimate__c":null,"No_of_Specialist_Tagsa__c":2,"No_of_ClinGen_records__c":0,"No_of_GeneReviews__c":0,"No_of_HHS_records__c":0,"World_Estimate__c":null,"No_of_HRSA_records__c":0,"Evidence_Based_Score__c":0,"No_of_Disease_Descriptions__c":3,"Disease_Characteristics_Score__c":2,"No_of_Age_at_Onset__c":0,"Description_Source__c":"MONDO:0005817","Disease_Description__c":"Kluver Bucy syndrome is a rare behavioral impairment characterized by inappropriate sexual behaviors and mouthing of objects. Other signs and symptoms include diminished ability to visually recognize objects,loss of normal fear and anger responses, memory loss, distractibility, seizures, and dementia. It is associated with damage to the anterior temporal lobes of the brain. Cases have been reported in association with herpes encephalitis and head trauma. Treatment is symptomatic and may include the use of psychotropic medications.","GARD_Name__c":"Kluver-Bucy syndrome","GARD_Synonym__c":"klver-bucy syndrome; klüver-bucy syndrome","Curated_Disease_Description_Source__c":"GARD:0006840","Curated_Disease_Description__c":"Kluver Bucy syndrome is a rare behavioral impairment characterized by inappropriate sexual behaviors and mouthing of objects. Other signs and symptoms, include a diminished ability to visually recognize objects, loss of normal fear and anger responses, memory loss, distractibility, seizures, and dementia. It is associated with damage to the anterior temporal lobes of the brain. Cases have been reported in association with herpes encephalitis and head trauma.","Curated_USA_Estimate_Source__c":null,"Curated_USA_Estimate__c":null,"Age_at_Onset_Snippet_Text__c":null,"SourceID__c":"ORPHA:157823","Deprecated__c":"No","Disease_Concept_Type__c":"Rare Disease Entity","MONDO_ID__c":"MONDO:0005817","ORPHANET_ID__c":"ORPHA:157823","Replaced_By_ID__c":null,"Display_Spanish_Disease_Name__c":"Síndrome de klüver-bucy","Spanish_Description_Source__c":null,"Spanish_Description__c":null,"Spanish_Disease_Name__c":"síndrome de klüver-bucy","Spanish_GARD_Synonym__c":null,"Category_Linearization__c":"ORPHA:98006","icd10_id__c":null,"mesh_id__c":null,"omim_id__c":null,"snomed_id__c":null,"umls_id__c":null,"GARD_Disease__c":[{"Curated_Disease_Description__c":"Kluver Bucy syndrome is a rare behavioral impairment characterized by inappropriate sexual behaviors and mouthing of objects. Other signs and symptoms, include a diminished ability to visually recognize objects, loss of normal fear and anger responses, memory loss, distractibility, seizures, and dementia. It is associated with damage to the anterior temporal lobes of the brain. Cases have been reported in association with herpes encephalitis and head trauma.","Curated_Disease_Description_Source__c":"GARD:0006840","GARD_Synonym__c":"klver-bucy syndrome; klüver-bucy syndrome","Name":"Kluver-Bucy syndrome","estimateUsa":""}],"GARD_Disease_Tag__c":[{"Tag_Name__c":"Neurology","Tag_Category__c":"Disease Category;Specialist","category_description":"Neurological diseases affect the brain, spinal cord, cranial nerves, autonomic nerves, or other peripheral nerves.","curated_tag_name":"Neurological diseases"},{"Tag_Name__c":"Psychiatry","Tag_Category__c":"Specialist"}],"External_Identifier_Disease__c":[{"URL__c":"https://uts.nlm.nih.gov/uts/umls/concept/C0270707","Source__c":"C0270707","Xref__c":"C0270707"},{"URL__c":"https://www.ebi.ac.uk/ols4/ontologies/doid/classes?obo_id=DOID%3A2510","Source__c":"MONDO:0005817","Xref__c":"DOID:2510"},{"URL__c":"https://www.ncbi.nlm.nih.gov/mesh/C020232","Source__c":"C0270707; MONDO:0005817","Xref__c":"D020232"},{"URL__c":"https://evsexplore.semantics.cancer.gov/evsexplore/concept/ncit/C84802","Source__c":"C0270707; MONDO:0005817","Xref__c":"C84802"},{"URL__c":"https://www.ncbi.nlm.nih.gov/medgen/?term=124361","Source__c":"C0270707","Xref__c":"MEDGEN:124361"},{"URL__c":"https://browser.ihtsdotools.org/?perspective=full&conceptId1=10651001","Source__c":"MONDO:0005817","Xref__c":"10651001"},{"URL__c":"https://www.orpha.net/en/disease/detail/157823","Source__c":"C0270707; MONDO:0005817; ORPHA:157823","Xref__c":"ORPHA:157823"},{"URL__c":"http://purl.obolibrary.org/obo/MONDO_0005817","Source__c":"GARD:0006840","Xref__c":"MONDO:0005817"}],"tags":{"Disease Category":["Neurology"],"Specialist":["Neurology","Psychiatry"]},"synonyms":["klver-bucy syndrome"," klüver-bucy syndrome"]}