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Cor triatriatum sinister


Title


Other Names:
Cor triatriatum sinistrum; Divided left atrium
Categories:
Congenital and Genetic Diseases; Heart Diseases

Summary Summary


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Cor triatriatum sinister (CTS) results when the left atrium is divided into two compartments by a membrane. The membrane can vary in size and shape and may have one or more openings.[1] Severe cases of cor triatriatum sinister usually present in infancy and are often associated with other heart defects. In less severe cases, the diagnosis may not be made until later in life.[1][2] The specific symptoms depend on the degree to which the membrane obstructs the flow of blood and whether or not there are additional heart defects.[1][2] Symptoms may range from mild shortness of breath during exercise to signs of heart failure and lung congestion. Some people with CTS may not have symptoms.[1][2] Treatment varies according to the severity of the symptoms. For symptomatic patients, surgery is generally considered the definitive course of therapy.[2][3]
Last updated: 11/11/2015

Treatment Treatment


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Treatment for cor triatriatum sinister varies depending on the symptoms. For patients with milder cases who are diagnosed much later in life, surgery may not be needed. [2] In symptomatic patients, treatment may include diuretics, medications to change the force of the heart's contractions (inotropic medications), and medications to prevent clots from forming (anticoagulant therapy).[2][1] Surgery, however, is considered the definitive therapy for those who are symptomatic.[2][3] The overall life expectancy after surgical repair is expected to be similar to that for the general population.[4]
Last updated: 11/11/2015
Do you have updated information on this disease? We want to hear from you.

Organizations Organizations


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Support and advocacy groups can help you connect with other patients and families, and they can provide valuable services. Many develop patient-centered information and are the driving force behind research for better treatments and possible cures. They can direct you to research, resources, and services. Many organizations also have experts who serve as medical advisors or provide lists of doctors/clinics. Visit the group’s website or contact them to learn about the services they offer. Inclusion on this list is not an endorsement by GARD.

Organizations Supporting this Disease

  • American Heart Association
    7272 Greenville Avenue
    Dallas, TX 75231-4596
    Toll-free: 800-242-8721
    Telephone: 214-373-6300
    Fax: 214-373-0268
    E-mail: Review.personal.info@heart.org
    Website: http://www.heart.org/
  • Congenital Heart Information Network (C.H.I.N.)
    101 N Washington Ave, Suite 1A
    Margate City, NJ 08402-1195
    Telephone: 609-822-1572
    Fax: 609-822-1574
    E-mail: mb@tchin.org
    Website: http://www.tchin.org
  • The Children's Heart Foundation
    PO Box 244
    Lincolnshire, IL 60069-0244
    Toll-free: 888-248-8140
    Telephone: 847-634-6474
    E-mail: info@childrensheartfoundation.org
    Website: http://www.childrensheartfoundation.org/
Do you know of an organization? We want to hear from you.

Learn More Learn More


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These resources provide more information about this condition or associated symptoms. The in-depth resources contain medical and scientific language that may be hard to understand. You may want to review these resources with a medical professional.

Where to Start

  • The National Organization for Rare Disorders (NORD) has a report for patients and families about this condition. NORD is a patient advocacy organization for individuals with rare diseases and the organizations that serve them.

In-Depth Information

  • Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free.
  • The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers. Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition.
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Cor triatriatum sinister. Click on the link to view a sample search on this topic.

News & Events News & Events


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News

  • National DNA Day Reddit "Ask Me Anything" (AMA) Series
    April 11, 2018

Related Diseases Related Diseases


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The following diseases are related to Cor triatriatum sinister. If you have a question about any of these diseases, you can contact GARD.

  • Cor triatriatum

GARD Answers GARD Answers


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Questions sent to GARD may be posted here if the information could be helpful to others. We remove all identifying information when posting a question to protect your privacy. If you do not want your question posted, please let us know.

Have a question? Contact a GARD Information Specialist.

References References


  1. Shirani, Jamshid. Cor Triatriatum. Medscape Reference. December 18, 2014; http://emedicine.medscape.com/article/154168-overview. Accessed 11/11/2015.
  2. Strickland, PT et al.. Cor triatriatum sinister: a patient, a review, and some unique findings.. Echocardiography. July, 2014; 31(6):790-4. http://www.ncbi.nlm.nih.gov/pubmed/?term=24649916. Accessed 11/11/2015.
  3. Saxena, P et al.. Surgical repair of cor triatriatum sinister: the Mayo Clinic 50-year experience. Annals of Thoracic Surgery. May, 2014; 97(5):1659-63. http://www.ncbi.nlm.nih.gov/pubmed/?term=24630764. Accessed 11/11/2015.
  4. Capdeville, Michelle, et al.. Cor Triatriatum Sinister Presenting in Adulthood. Journal of Cardiothoracic and Vascular Anesthesia. April, 2014; 28(2):408-16. http://www.ncbi.nlm.nih.gov/pubmed/24355595. Accessed 11/11/2015.
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