In addition to the port wine stain and pigmentary lesions, other skin lesions are not uncommon, such as:
Nevus of Ota
Nevus of Ito
Around half of people with PPV have systemic involvement (i.e., other body systems are affected). Eye conditions such as ocular melanosis (also called ocular melanocytosis) is common. Ocular melanosis refers to a blue-gray pigmentation in the 'white of the eye' or sclerae. This condition often occurs along with nevus of Ota and may affect one or both eyes. The complications of nevus of Ota are
Some individuals with PPV also have Sturge-Weber
You can learn more about Sturge-Weber syndrome on our Web site at the following link:
You can learn more about Klippel-Trenaunay syndrome on the Genetic Home Reference Web site at the following link:
Support and advocacy groups can help you connect with other patients and families, and they can provide valuable services. Many develop patient-centered information and are the driving force behind research for better treatments and possible cures. They can direct you to research, resources, and services. Many organizations also have experts who serve as medical advisors or provide lists of doctors/clinics. Visit the group’s website or contact them to learn about the services they offer. Inclusion on this list is not an endorsement by GARD.
These resources provide more information about this condition or associated symptoms. The in-depth resources contain medical and scientific language that may be hard to understand. You may want to review these resources with a medical professional.
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My son has been diagnosed with phacomatosis pigmentovascularis. Can you provide me with further information on this condition? See answer