In individuals with NF2, the most common tumors are called vestibular schwannomas (also called acoustic neuromas). These tumors develop along the nerve that carries information from the inner ear to the brain (the auditory nerve). Tumors that occur on nerves in other areas of the brain or spinal cord are also commonly seen in individuals with NF2. In schwannomatosis, multiple schwannomas can develop from nerves of the head, spine, or limbs, but there are no vestibular schwannomas as seen in NF2. In both of these disorders, various other signs and symptoms are typically present.
Another condition in which schwannomas may occur is called Carney complex. Carney complex is a disorder characterized by an increased risk of several types of tumors. Affected individuals usually have changes in skin coloring (pigmentation). Individuals with Carney complex are at increased risk of developing benign tumors called myxomas in the heart and other parts of the body; tumors in hormone-producing (endocrine) glands such as the adrenal glands, as well as the thyroid, testes, and ovaries; and a rare tumor called psammomatous melanotic schwannoma.
Last updated: 3/9/2015
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