is a rare condition that occurs when the walls of the airway (specifically the trachea
) are weak. This can cause the airway to become narrow or collapse.
There are two forms of TBM: a congenital form (called primary TBM) that typically develops during infancy or early childhood and an acquired form (called secondary TBM) that is usually seen in adults.
Some affected people may initially have no signs or symptoms. However, the condition is typically progressive (becomes worse overtime) and most people will eventually develop characteristic features such as shortness of breath, cough, sputum retention (inability to clear mucus from the respiratory tract), and wheezing or stridor
Most cases of primary TBM are caused by genetic conditions that weaken the walls of the airway, while the secondary form often occurs incidentally due to trauma, chronic inflammation and/or prolonged compression of the airways.
Treatment is generally only required in those who have signs and symptoms of the condition and may include stenting
, surgical correction, continuous positive airway pressure (CPAP)
, and tracheostomy
Last updated: 3/6/2015