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soft tissue of the fingers, hands and forearms of young adults. It may also be found in the legs, trunk, head or neck regions. It is rare in young children and adults, and it occurs more frequently in men. Epithelioid sarcoma begins as a painless, firm growth or bump that may be accompanied by an open wound (ulceration) in the skin covering the growth. It is considered an aggressive cancer because it has a high chance of regrowing after treatment (a recurrence), or spreading to surrounding tissues or more distant parts of the body (a metastasis). Epithelioid sarcoma is first treated with surgery to remove all the cancer cells (wide local excision). Amputation of part of the affected limb may be needed in severe cases. Radiation therapy or chemotherapy may also be used to destroy any cancer cells not removed during surgery.Epithelioid sarcoma is a rare cancer that most often occurs in the
Last updated: 9/16/2011
- Nagoshi N, Anazawa U, Morioka H, Mukai M, Yabe H, Toyama Y. Epithelioid sarcoma arising on the forearm of a 6-year-old boy: case report and review of the literature. Pediatric Surgery International. 2006; 22:771-773. http://www.ncbi.nlm.nih.gov/pubmed/16786373. Accessed 9/13/2011.
- Pai KK, Pai SB, Sripathi H, Pranab, Rao P. Epithelioid sarcoma: a diagnostic challenge. Indian Journal of Dermatology, Venereology and Leprology. 2006; 72:446-448. http://www.ncbi.nlm.nih.gov/pubmed/17179622. Accessed 9/13/2011.
- Armah HB, Parwani AV. Epithelioid Sarcoma. Archives of pathology & Laboratory Medicine. 2009; 133:814-819. http://www.ncbi.nlm.nih.gov/pubmed/19415960. Accessed 9/13/2011.
- The Liddy Shriver Sarcoma Initiative provides information on epithelioid sarcoma.
- The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers. Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition.
- PubMed is a searchable database of medical literature and lists journal articles that discuss Epithelioid sarcoma. Click on the link to view a sample search on this topic.