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Diseases

Genetic and Rare Diseases Information Center (GARD)

Camptocormism


Other Names for this Disease
  • Camptocormia
  • Bent spine
  • Bent Spine Syndrome
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Overview

Camptocormia, camptocormism or "bent spine syndrome," (BSS) is an extreme forward flexion of the thoracolumbar spine, which often worsens during standing or walking, but completely resolves when laying down. The term itself is derived from the Greek "kamptos" (to bend) and "kormos" (trunk) BSS was initially considered, especially in wartime, as a result of a psychogenic disorder. It is now recognized that in it may also be related to a number of musculo-skeletal or neurological disorders. It seems that myopathy is the primary cause of camptocormia based on electromyography, magnetic resonance imaging/computed tomography (CT/MRI scans) of paraspinal muscles, and muscle biopsy. The majority of BSS of muscular origin is related to a primary idiopathic (with unknwon cause) axial myopathy of late onset, maybe a delayed-onset paraspinal myopathy, appearing in elderly patients. Causes of secondary BSS are numerous. The main causes are muscular disorders like inflammatory myopathies, muscular dystrophies of late onset, myotonic myopathies, endocrine and metabolic myopathies, and neurological disorders, principally Parkinson’s disease. Diagnosis of axial myopathy is based upon CT/MRI scans demonstrating a lot of fatty infiltration of paravertebral muscles. General activity, walking with a cane, physiotherapy, and exercises should be encouraged. Treatment of secondary forms of BSS is dependent upon the cause.[1][2][3]
Last updated: 9/17/2015

References

  1. Ghosh PS & Milone M. Camptocormia as presenting manifestation of a spectrum of myopathic disorders. Muscle Nerve. 2015; http://onlinelibrary.wiley.com/doi/10.1002/mus.24689/full. Accessed 9/17/2015.
  2. Upadhyaya CD, Starr PA & Mummaneni PV. Spinal Deformity and Parkinson Disease: A Treatment Algorithm. Neurosurg Focus. August, 2010.; 28(3):E5:http://www.medscape.com/viewarticle/723141_2. Accessed 9/17/2015.
  3. Lenoir T, Guedj N, Boulu P, Guigui P & Benoist M. Camptocormia: the bent spine syndrome, an update. Eur Spine J. March 19, 2010; 19(8):1229–1237. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2989190/. Accessed 9/17/2015.
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In Depth Information

  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Camptocormism. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • Camptocormia
  • Bent spine
  • Bent Spine Syndrome
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.