Adult neuronal ceroid lipofuscinosis
Other Names for this Disease
- Adult NCL
- CLN4 disease, adult autosomal dominant
- Hagberg-Santavuori disease
- Autosomal recessive neuronal ceroid lipofuscinosis 4A
- Neuronal ceroid lipofuscinosis
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Your QuestionIs Kuf's a terminal disease?
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The symptoms of adult neuronal ceroid lipofuscinosis get worse over time, and this condition shortens a persons life expectancy. Most sources state that a person with adult neuronal ceroid lipofuscinosis usually lives about 10 years after the symptoms begin.
Last updated: 11/29/2012
- Batten Disease Fact Sheet. National Institute of Neurological Disorders and Stroke. October 18, 2012; http://www.ninds.nih.gov/disorders/batten/detail_batten.htm#220083063. Accessed 11/29/2012.
- Kufs disease. Genetics Home Reference. September 2010; http://ghr.nlm.nih.gov/condition/kufs-disease. Accessed 11/29/2012.
- Mole SE, Williams RE. Neuronal Ceroid-Lipofuscinoses. GeneReviews. March 2, 2010; http://www.ncbi.nlm.nih.gov/books/NBK1428/. Accessed 11/29/2012.