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Diseases

Genetic and Rare Diseases Information Center (GARD)

Autosomal dominant neuronal ceroid lipofuscinosis 4B


Other Names for this Disease
  • CLN4B
  • Kuf's disease, autosomal dominant
  • Ceroid lipofuscinosis, neuronal, Parry type
  • Ceroid lipofuscinosis, neuronal, 4B, autosomal dominant
  • Neuronal ceroid lipofuscinosis 4B
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Your Question

Is Kuf's a terminal disease?

Our Answer

We have identified the following information that we hope you find helpful. If you still have questions, please contact us.

What is the long-term outlook for people with adult neuronal ceroid lipofuscinosis?

Unfortunately, the long-term outlook (prognosis) for people with adult neuronal ceroid lipofuscinosis is generally poor. The symptoms tend to become worse over time, resulting in a shortened life expectancy. Most sources state that a person with adult neuronal ceroid lipofuscinosis usually lives about 10 years after the symptoms begin.[1][2]
Last updated: 8/31/2015

References
Other Names for this Disease
  • CLN4B
  • Kuf's disease, autosomal dominant
  • Ceroid lipofuscinosis, neuronal, Parry type
  • Ceroid lipofuscinosis, neuronal, 4B, autosomal dominant
  • Neuronal ceroid lipofuscinosis 4B
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.