Dysplasia epiphysealis hemimelica
Other Names for this Disease
- Trevor disease
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 Early diagnosis and treatment are necessary to prevent joint dysfunction and deformity and may be surgical or non-surgical depending on the location and the symptoms. Due to the progressive nature of this disorder and the chance of worsening deformity, patients should be followed until skeletal maturity. The cause of dysplasia epiphysealis hemimelica is not known.Dysplasia epiphysealis hemimelica (DEH), or Trevor's disease, is a rare condition that most commonly affects the epiphysis (the end) of long bones in children.
Last updated: 5/10/2011
- Wenger DR, Adamczk MJ. Evaluation, imaging, histology and operative treatment for dysplasia epiphysealis hemimelica (Trevor disease) of the acetabulum: a case report and review. Iowa Orthop J. 2005; http://www.ncbi.nlm.nih.gov/pubmed/16089075. Accessed 5/10/2011.
- Glick R, Khaldi L, Ptaszynski K, Steiner GC. Dysplasia epiphysealis hemimelica (Trevor disease): a rare developmental disorder of bone mimicking osteochondroma of long bones. Hum Pathol. 2007; http://www.ncbi.nlm.nih.gov/pubmed/17490719. Accessed 5/10/2011.
- Rosero VM, Kiss S, Terebessy T, Kollo K, Szoke G. Dysplasia epiphysealis hemimelica (Trevor's disease): 7 of our own cases and a review of the literature. Acta Orthop. 2007; http://www.ncbi.nlm.nih.gov/pubmed/18236195. Accessed 5/10/2011.
- Douira-Khomsi W, Louati H, Mormech Y, et al.. Dysplasia epiphysealis hemimelica: a report of four cases. Foot Ankle Surg. 2011; http://www.ncbi.nlm.nih.gov/pubmed/21276564. Accessed 5/10/2011.
- Smith EL, Raney EM, Matzkin EG, Fillman RR, Yandow SM. Trevor's disease: the clinical manifestations and treatment of dysplasia epiphysealis hemimelica. J Pediatr Orthop B. 2007; http://www.ncbi.nlm.nih.gov/pubmed/17527110. Accessed 5/10/2011.
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