Jervell Lange-Nielsen syndrome
Other Names for this Disease
- Deafness, congenital, and functional heart disease
- Prolonged QT interval in EKG and sudden death
- Cardioauditory syndrome of Jervell and Lange-Nielsen
- Surdo-cardiac syndrome
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long QT syndrome. Symptoms include deafness from birth, arrhythmia, fainting, and sudden death. There are two different types, Jervell Lange-Nielsen syndrome type 1 and 2. It is inherited in an autosomal recessive fashion.Jervell Lange-Nielsen syndrome is a form of
Last updated: 12/18/2008
- Sovari AA, Kocheril AG, Assadi R Baas AS, Zareba W, Rosero S. Long QT syndrome. eMedicine. 2010; http://emedicine.medscape.com/article/157826-overview . Accessed 4/15/2011.
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- Identification and Treatment of Sudden Death Conditions in Young Patients. A presentation by David Bradley, M.D., Director, Pediatric Heart Rhythm Service, CS Mott Children's Hospital. Assoicate Professor, Department of Pediatrics and Communicable Diseases, University of Michigan.