Other Names for this Disease
- Congenital tracheobronchomegaly
- Idiopathic tracheobronchomegaly
- Mounier Kuhn syndrome
- Mounier-Kühn syndrome
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lung function tests, bronchoscopy, and a chest CT scan. The cause of Mounier-Kuhn syndrome is unknown, although cigarette smoke and air pollutants may act as irritating factors. Some cases are associated with connective tissue diseases such as Ehlers-Danlos syndrome, Marfan syndrome, and cutis laxa and may be inherited. Treatment typically involves chest physical therapy and antibiotics to treat infections.Mounier-Kuhn syndrome is a lung disorder that causes the respiratory tract to dilate or enlarge. People with this condition develop frequent respiratory tract infections and recurrent cough. The condition can be diagnosed by
Last updated: 8/5/2015
- Celik B, Bilgin S, Yuksel C. Mounier-Kuhn Syndrome: A Rare Cause of Bronchial Dilation. Texas Heart Institute Journal. 2011; 38(2):194-196. http://www.ncbi.nlm.nih.gov/pmc/articles/pmid/21494536/. Accessed 8/5/2015.
- Cordier JF, Cottin V, Lazor R, Prevot G. Mounier-Kühn syndrome. Orphanet. April 2014; http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3347. Accessed 8/5/2015.
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- Online Mendelian Inheritance in Man (OMIM) is a catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine.
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