Paget disease, extramammary
Other Names for this Disease
- Extramammary Paget disease
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eczema-like rash of the skin around the genital regions of males and females. Under the microscope, this condition looks very similar to a condition that occurs on the breast called mammary Paget disease. The primary difference between the two is the location of the rash. While the location of the rash for individuals with mammary Paget disease is around the nipple and areolar skin, EPMD may occur in the vulva, perianal region, scrotum, penis, and axilla. EPMD most often occurs in women between age 50 to 60. About 25 percent of extramammary Paget disease is associated with an underlying cancer. Treatment typically includes surgery. Prognosis varies depending on how early the disorder was diagnosed and treated as well as the association with an underlying cancer. Extramammary Paget disease (EPMD) is characterized by a chronic
Last updated: 3/8/2016
- Extramammary Paget Disease. New Zealand Dermatological Society. September 2015; http://dermnetnz.org/site-age-specific/extra-mammary-paget.html.
- Sandu N, Schwartz RA. Extramammary Paget disease. Medscape Reference. October 3, 2014; http://emedicine.medscape.com/article/1100397-overview.
- DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
- Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free.
- The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers. Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition.
- Online Mendelian Inheritance in Man (OMIM) is a catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine.
- Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
- PubMed is a searchable database of medical literature and lists journal articles that discuss Paget disease, extramammary. Click on the link to view a sample search on this topic.