Progressive deafness with stapes fixation
Other Names for this Disease
- Thies Reis syndrome
- Thies-Reis syndrome
- Stapedo-vestibular ankylosis
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Treatment for deafness, progressive with stapes fixation typically involves surgery. The conductive component of the hearing loss can be restored by surgery or hearing aids. The associated sensorineural component is managed by hearing aids or cochlear implants, depending on its severity. Stapedotomy (a procedure where a laser is used to make a hole in the stapes) or partial stapedectomy (removal of the stapes) with stapes replacement using a prostheses most commonly achieves satisfactory results with minimal complications.
Last updated: 12/11/2009
- Deafness, Progressive, with Stapes Fixation. Online Mendelian Inheritance in Man (OMIM). 1996; http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=601449. Accessed 12/11/2009.
- Bozorg Grayeli A. Deafness, progressive, with stapes fixation. Orphanet. 2006; http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=3235. Accessed 12/11/2009.
- Albert S, Roger Gm Rouillon I, Chauvin P, Denoyelle F, Derbez R, Delattre J, Triglia JM, Garabedian EN. Laryngoscope. 2006; http://www.ncbi.nlm.nih.gov/pubmed/16826051. Accessed 12/11/2009.
- Salahuddin I, Salahuddin A. Ear Nose Throat. 2002; http://www.ncbi.nlm.nih.gov/pubmed/12199172. Accessed 12/11/2009.
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