Hereditary neuropathy with liability to pressure palsy
- Polyneuropathy, familial recurrent
- Tomaculous neuropathy
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There is no specific treatment for hereditary neuropathy with liability to pressure palsy. Treatment is based on an individual's symptoms. Some people with this condition use braces, such as a wrist splint or ankle-foot orthosis (AFO). Protective pads worn at the elbows or knees may prevent pressure and trauma to local nerves. Activities to avoid include prolonged sitting with legs crossed, occupations requiring repetitive movements of the wrist, prolonged leaning on elbows, and rapid weight loss. Vincristine, commonly used in the treatment of lymphoma, has been reported to worsen the symptoms of hereditary neuropathy with liability to pressure palsy. Surgical decompression of nerves remains a controversial treament for this condition.
- Bird TD. Hereditary Neuropathy with Liability to Pressure Palsies. GeneReviews. September 25, 2014; http://www.ncbi.nlm.nih.gov/books/NBK1392/. Accessed 7/24/2015.
- GeneReviews provides current, expert-authored, peer-reviewed, full-text articles describing the application of genetic testing to the diagnosis, management, and genetic counseling of patients with specific inherited conditions.
- ClinicalTrials.gov lists trials that are studying or have studied Hereditary neuropathy with liability to pressure palsy. Click on the link to go to ClinicalTrials.gov to read descriptions of these studies.
- Orphanet lists European clinical trials, research studies, and patient registries enrolling people with this condition.