* Not a rare disease
Other Names for this Disease
- Nonimmune chronic idiopathic neutropenia of adults
severe chronic neutropenia whose cause is unknown. Neutropenia is a blood condition that causes a reduced number or complete absence of neutrophils, a type of white blood cell that is responsible for much of the body's protection against infection. Symptoms include fever, moth sores, and other types of infections. Neutropenia idiopathic may occur in children and adults. Frequency and severity of infections appear to be directly related to neutrophil count; while clinical problems in individual patients may vary, in general, those patients with more severe neutropenia have more frequent infections. Most patients respond well to granulocyte-colony stimulating factor (G-CSF). Long-term treatment is usually required.Idiopathic neutropenia is an acquired form of
Last updated: 1/13/2014
- Boxer, LA. Severe Combined Neutropenia. National Organization for Rare Disorders (NORD). 2012; http://www.rarediseases.org/rare-disease-information/rare-diseases/byID/857/viewAbstract. Accessed 1/13/2014.
- Types of neutropenia. National Neutropenia Network. 2014; http://www.neutropenianet.org/what-is-neutropenia/types-of-neutropenia/. Accessed 1/13/2014.
- Idiopathic Neutropenia. The Severe Chronic Neutropenia International Registry. http://depts.washington.edu/registry/Info.Idiopathic.Neut.htm. Accessed 1/13/2014.
- Treatment. National Neutropenia Network. 2014; http://www.neutropenianet.org/medical-care/treatment/. Accessed 1/13/2014.
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