Hyperlipoproteinemia type 1
Other Names for this Disease
- Hyperlipoproteinemia type I
- Lipoprotein lipase deficiency
- LPL deficiency
- Lipase D deficiency
- Hyperchylomicro-nemia familial
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Treatment for hyperlipoproteinemia type 1 is intended to control blood triglyceride levels with a very low-fat diet. It is recommended that individuals with this condition eat no more than 20 grams of fat per day. Medium-chain fatty acids (such as coconut oil) can be incorporated into the diet, as they are absorbed by the body in a different manner. Dietary counseling may be helpful to maintain adequate calorie and nutrient intake.
Last updated: 3/8/2016
- Martin LJ, Zieve D. Familial lipoprotein lipase deficiency. MedlinePlus. April 30, 2015; http://www.nlm.nih.gov/medlineplus/ency/article/000408.htm.
- Brunzell JD. Familial Lipoprotein Lipase Deficiency. GeneReviews. April 24, 2014; http://www.ncbi.nlm.nih.gov/books/NBK1308/.
- GeneReviews provides current, expert-authored, peer-reviewed, full-text articles describing the application of genetic testing to the diagnosis, management, and genetic counseling of patients with specific inherited conditions.