Hyperlipoproteinemia type 1
Other Names for this Disease
- Chylomicronemia syndrome
- Chylomicronemia, familial
- Familial chylomicronemia
- Hyperchylomicro-nemia familial
- Hyperlipemia idiopathic Burger-Grutz type
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Treatment for hyperlipoproteinemia type 1 is intended to control blood triglyceride levels with a very low-fat diet. Fat intake usually must be less than 20 grams per day to prevent symptoms. Medium-chain fatty acids (such as coconut oil) can be incorporated into the diet, as they are absorbed by the body in a different manner. Dietary counseling may be helpful to maintain adequate calorie and nutrient intake.
Last updated: 8/24/2009
- Brunzell JD. Familial Lipoprotein Lipase Deficiency. Gene Reviews. July 28, 2009; http://www.ncbi.nlm.nih.gov/bookshelf/br.fcgi?book=gene&part=lpl. Accessed 8/24/2009.
- Finding Treatment Information - A video developed by GARD Information Specialists that explains how you can find information about treatment for a rare disease.
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