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Diseases

Genetic and Rare Diseases Information Center (GARD)

Hereditary fructose intolerance


Other Names for this Disease
  • ALDOB deficiency
  • Aldolase B deficiency
  • Fructose intolerance, hereditary
  • Fructose-1,6-bisphosphate aldolase B deficiency
  • Fructose-1-phosphate aldolase deficiency
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Treatment

Newline Maker

How is hereditary fructose intolerance (HFI) treated?

Complete elimination of fructose and sucrose from the diet is an effective treatment for most people,[1] although this can be challenging. More information on treatment for HFI is available from the HFI Laboratory at Boston University at the following link. This page includes information on what people with HFI can and cannot eat.
http://www.bu.edu/aldolase/HFI/treatment/

Additional information on foods to avoid if you have HFI is available from the Mayo clinic.
http://www.mayoclinic.com/health/fructose-intolerance/AN01574
Last updated: 8/21/2015

References
  1. Haldeman-Englert C. Hereditary fructose intolerance. Medline Plus. May 2, 2013; http://www.nlm.nih.gov/medlineplus/ency/article/000359.htm. Accessed 8/20/2015.


GARD Video Tutorial

  • Finding Treatment Information - A video developed by GARD Information Specialists that explains how you can find information about treatment for a rare disease.

    Finding Treatment Information

Clinical Trials & Research for this Disease

  • ClinicalTrials.gov lists trials that are studying or have studied Hereditary fructose intolerance. Click on the link to go to ClinicalTrials.gov to read descriptions of these studies.
  • More information on research for hereditary fructose intolerance is available from the HFI Laboratory at Boston University.
  • Orphanet lists European clinical trials, research studies, and patient registries enrolling people with this condition. 
Other Names for this Disease
  • ALDOB deficiency
  • Aldolase B deficiency
  • Fructose intolerance, hereditary
  • Fructose-1,6-bisphosphate aldolase B deficiency
  • Fructose-1-phosphate aldolase deficiency
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.