Other Names for this Disease
- Apple peel small bowel syndrome
- Apple peel syndrome
- Apple-peel intestinal atresia
- Familial apple peel jejunal atresia
birth defect that occurs when the membrane that attaches the small intestines to the abdominal wall (called the mesentery) is partially or completely absent. As a result, a portion of the small intestines (the jejunum) twists around an artery that supplies blood to the colon (the marginal artery). This leads to an intestinal blockage or "atresia." Common symptoms include feeding difficulties, failure to thrive, vomiting bile (a bitter-tasting yellowish-green fluid), abdominal swelling, and/or absence of bowel movements after birth. It typically occurs sporadically in people with no family history of the condition; however, more than one family member can rarely be affected, suggesting that there may be a genetic component in some cases. Jejunal atresia is typically treated with surgery.Jejunal atresia is a
Last updated: 6/14/2015
- David E Wesson, MD. Intestinal atresia. UpToDate. June 2014; Accessed 6/12/2015.
- Biren P Modi, MD. Intestinal Atresia, Stenosis, and Webs. Medlineplus. December 2014; http://emedicine.medscape.com/article/940615-overview#aw2aab6b2.
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