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Diseases

Genetic and Rare Diseases Information Center (GARD)

Pseudomyxoma peritonei


Other Names for this Disease
  • PMP
  • Syndrome of pseudomyxoma peritonei
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Overview

Pseudomyxoma peritonei (PMP) is a rare condition characterized by the presence of mucin in the abdominal (peritoneal) cavity. While the most common cause of PMP is appendix cancer, several types of tumors (including non-cancerous tumors) can cause PMP.[1] Signs and symptoms may include an increase in abdominal size or bloating; inguinal hernia (in men); an ovarian mass, felt during a routine pelvic exam (in women); pain or discomfort in the abdomen; and/or appendicitis.[2][1] Treatment depends on the underlying cause of the condition (the location and type of the original tumor, including whether it is malignant) and the extent of spreading.[1] It may involve surgically removing as much of the tumor as possible (debulking); radiotherapy; and/or chemotherapy.[1][2]
Last updated: 4/11/2016

References

  1. About ACPMP. ACPMP Research Foundation. http://acpmp.org/about-acpmp.
  2. Richard Swanson, Jeffrey A Meyerhardt. Cancer of the appendix and pseudomyxoma peritonei. UpToDate. Waltham, MA: UpToDate; March, 2016;
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Basic Information

  • The Appendix Cancer/Pseudomyxoma Peritonei Research Foundation has a list of frequently asked questions for those diagnosed with Pseudomyxoma Peritonei (PMP), Appendix Cancer and related Peritoneal Surface Malignancies (PSM), and their caregivers. Click on the link above to view their answers to these questions.
  • Cancer Research UK provides a basic overview of Pseudomyxoma peritonei on their website.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.
  • Pseudomyxoma Survivor is a support network for those affected by PMP, appendix cancer and peritoneal surface malignancies. Click on the link above to view information about Pseudomyxoma peritonei.

In Depth Information

  • The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers. Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition.
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Pseudomyxoma peritonei. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • PMP
  • Syndrome of pseudomyxoma peritonei
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.